Fatal interstitial pulmonary fibrosis in anti-Jo-1-negative amyopathic dermatomyositis

被引:23
作者
High, WA [1 ]
Cohen, JB [1 ]
Murphy, BA [1 ]
Costner, MI [1 ]
机构
[1] Univ Texas, SW Med Ctr, Dept Dermatol, Dallas, TX 75390 USA
关键词
D O I
10.1067/S0190-9622(03)01482-8
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 [皮肤病与性病学];
摘要
Amyopathic dermatomyositis (DM) describes a subpopulation with the cutaneous eruption of DM, but without muscle involvement. Interstitial pulmonary fibrosis is a recognized complication of DM, often correlated with antisynthetase enzymes, such as anti-Jo-1. We describe a case of fatal IPF in a patient with anti-Jo-1 antibody-negative amyopathic DM.
引用
收藏
页码:295 / 298
页数:4
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