Waldenstrom's macroglobulinemia with pulmonary amyloidosis

被引:2
作者
Zatloukal, P
Bezdicek, P
Schimonová, M
Havlicek, F
Tesarová, P
Slováková, A
机构
[1] Charles Univ, Fac Med 3, Dept Pneumol & Thorac Surg, Prague 18081 8, Czech Republic
[2] Charles Univ, Fac Med 1, Dept TB & Resp Dis Pathol & Hematol 1, Prague, Czech Republic
关键词
monoclonal gammopathy; pulmonary amyloidosis; Waldenstrom's macroglobulinemia;
D O I
10.1159/000029306
中图分类号
R56 [呼吸系及胸部疾病];
学科分类号
摘要
We present a case of AL-type amyloidosis involving pulmonary parenchyma and hilar and mediastinal lymph nodes in a patient with Waldenstrom's macroglobulinemia. Direct infiltration of pulmonary parenchyma by lymphocytes and plasma cells is an important factor in the etiology and pathogenesis of pulmonary manifestations of the disease. Despite detailed examination, eve did not find amyloid depositions in any extrapulmonary site.
引用
收藏
页码:414 / 416
页数:3
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