Primary cardiac lymphoma in an immunocompetent woman

被引:7
作者
Begueret, H [1 ]
Labouyrie, E [1 ]
Dubus, P [1 ]
Sempe, S [1 ]
Goussot, JF [1 ]
Besse, P [1 ]
De Mascarel, A [1 ]
Merlio, JP [1 ]
机构
[1] Hop Haut Leveque, Dept Pathol, Bordeaux, France
关键词
cardiac lymphoma; immunocompetent; phenotype; Polymerase Chain Reaction;
D O I
10.3109/10428199809059237
中图分类号
R73 [肿瘤学];
学科分类号
100214 ;
摘要
We report a fatal primary cardiac non-Hodgkin's lymphoma in a 62 years old immunocompetent woman presenting with tamponade and complete atrioventricular block. CT-scan, echocardiography and autopsy examination showed a tumor largely infiltrating the heart without extracardiac involvement. A surgical biopsy revealed high grade B-cell non-Hodgkin's lymphoma with a misleading myelomonocytic CD68 (KP1) expression. Polymerase Chain Reaction analysis revealed a clonal rearrangement of the immunoglobulin heavy chain gene and confirmed the B-cell origin of the lymphoma. Our report also emphasizes the role of immunohistochemical and molecular techniques in the diagnosis.
引用
收藏
页码:423 / 428
页数:6
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