MELAS exhibits dominant negative effects on mitochondrial RNA processing

被引:7
作者
Koge, Y [1 ]
Yoshino, M [1 ]
Kato, H [1 ]
机构
[1] Kurume Univ, Sch Med, Dept Pediat & Child Hlth, Kurume, Fukuoka 830, Japan
关键词
D O I
10.1002/ana.410430620
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
引用
收藏
页码:835 / 835
页数:1
相关论文
共 5 条
[1]  
BINDOFF LA, 1993, J BIOL CHEM, V268, P19559
[2]   Mitochondrial DNA and RNA processing in MELAS [J].
Kaufmann, P ;
Koga, Y ;
Shanske, S ;
Hirano, M ;
DiMauro, S ;
King, MP ;
Schon, EA .
ANNALS OF NEUROLOGY, 1996, 40 (02) :172-180
[3]   DEFECTS IN MITOCHONDRIAL PROTEIN-SYNTHESIS AND RESPIRATORY-CHAIN ACTIVITY SEGREGATE WITH THE TRANSFER RNA(LEU)(UUR) MUTATION ASSOCIATED WITH MITOCHONDRIAL MYOPATHY, ENCEPHALOPATHY, LACTIC-ACIDOSIS, AND STROKE-LIKE EPISODES [J].
KING, MP ;
KOGA, Y ;
DAVIDSON, M ;
SCHON, EA .
MOLECULAR AND CELLULAR BIOLOGY, 1992, 12 (02) :480-490
[4]  
KOGA Y, 1995, MUSCLE NERVE, pS119
[5]  
MASUCCI JP, 1995, MOL CELL BIOL, V15, P2872