Secondary nephropathic amyloidosis in cystic fibrosis

被引：3

作者：

Guillot, M

Drut-Desombre, B

Amiour, M

Aljazayri, Z

Eckart, P

Dominique, S

Grateau, G

机构：

[1] Ctr Hosp Gen, Serv Pediat, F-14107 Lisieux, France

[2] Ctr Hosp Gen, Ctr Soins Mucoviscidose, F-14107 Lisieux, France

[3] CHU, Serv Pneumol, F-76031 Rouen, France

[4] Ctr Hosp Hotel Dieu, Serv Med Interne, F-75181 Paris 04, France

来源：

ARCHIVES DE PEDIATRIE | 1998年 / 5卷 / 08期

关键词：

amyloidosis; cystic fibrosis; kidney failure; chronic; adult;

D O I：

10.1016/S0929-693X(98)80133-4

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

Background. - Due to the improvement in cystic fibrosis management, life expectancy has risen; on the other hand, longer survival has led to new complications, including secondary renal amyloidosis, which has been so far very uncommonly reported. Case reports. - Secondary nephropathic amyloidosis was seen in two 25-year and 22-year-old adults with cystic fibrosis. Both had developed recurrent pulmonary infections due to Pseudomonas aeruginosa over several years. One patient died after 2 years of progressive kidney failure. Conclusion. - Severe renal insufficiency due to secondary amyloidosis may complicate the course of cystic fibrosis and become the main prognosis factor in adults. (C) 1998, Elsevier, Paris.

引用

页码：884 / 886

页数：3

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