Measuring Friedreich ataxia: Interrater reliability of a neurologic rating scale

被引:280
作者
Subramony, SH
May, W
Lynch, D
Gomez, C
Fischbeck, K
Hallett, M
Taylor, P
Wilson, R
Ashizawa, T
机构
[1] Univ Mississippi, Med Ctr, Dept Neurol, Jackson, MS 39216 USA
[2] Univ Mississippi, Med Ctr, Dept Prevent Med, Jackson, MS 39216 USA
[3] Childrens Hosp Philadelphia, Dept Neurol, Philadelphia, PA 19104 USA
[4] Univ Minnesota, Dept Neurol, Minneapolis, MN 55455 USA
[5] NINDS, Neurogenet Branch, NIH, Bethesda, MD 20892 USA
[6] Univ Penn, Dept Neurol, Philadelphia, PA 19104 USA
[7] Univ Penn, Dept Pathol, Philadelphia, PA 19104 USA
[8] Univ Texas, Med Branch, Dept Neurol, Galveston, TX 77555 USA
关键词
D O I
10.1212/01.WNL.0000156802.15466.79
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Measuring the severity of neurologic dysfunction in patients with inherited ataxias, including Friedreich ataxia (FA), is difficult because of the variable rate of progression, the variable age at onset and the variety of neural systems that may be affected. The authors discuss the problems related to rating scales in the ataxias, report a neurologic rating scale for FA, and demonstrate acceptable interrater reliability of the instrument.
引用
收藏
页码:1261 / 1262
页数:2
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