Japanese Biliary Atresia Registry

被引：127

作者：

Nio, Masaki ^{[1
]}

机构：

[1] Tohoku Univ, Grad Sch Med, Japanese Biliary Atresia Soc, Aoba Ku, 1-1 Seiryomachi, Sendai, Miyagi 9808574, Japan

来源：

PEDIATRIC SURGERY INTERNATIONAL | 2017年 / 33卷 / 12期

关键词：

Biliary atresia; Japanese registry; Kasai portoenterostomy; Liver transplantation; Long-term follow-up;

D O I：

10.1007/s00383-017-4160-x

中图分类号：

R72 [儿科学];

学科分类号：

100202 [儿科学];

摘要：

The Japanese Biliary Atresia Registry (JBAR) was launched in 1989 by the Japanese Biliary Atresia Society (JBAS). JBAR employed an initial questionnaire, a questionnaire for liver transplantation, and a follow-up questionnaire. The questionnaire has been sent to the pediatric surgeons of JBAS member institutions and the hospitals in which council members of the Japanese Society of Pediatric Surgeons are working. One hundred and twenty-three hospitals have been included in JBAR between 1989 and 2015. Each patient is to be followed up for 30 years. Between 1989 and 2015, 3160 patients have been registered in JBAR. Among them, 1236 patients underwent liver transplantation. Follow-up questionnaire is also going on. 20-year overall and native-liver survival rates were 89 and 49%, respectively. The surgical outcome of BA has markedly improved owing to the co-operation of Kasai portoenterostomy and liver transplantation. Japanese big database of BA is now available.

引用

页码：1319 / 1325

页数：7

共 26 条

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[10]

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