The coexistence of familial Mediterranean fever and polyarteritis nodosa; Report of a case

被引:20
作者
Kocak, H [1 ]
Cakar, N [1 ]
Hekimoglu, B [1 ]
Atakan, C [1 ]
Akkok, N [1 ]
Unal, S [1 ]
机构
[1] SOCIAL SECUR HOSP,DEPT PEDIAT NEPHROL,ANKARA,TURKEY
关键词
familial Mediterranean fever; polyarteritis nodosa;
D O I
10.1007/s004670050176
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
We describe a 14-year-old boy with a 5-year history of familial Mediterranean fever (FMF), treated with colchicine, who developed polyarteritis nodosa (PAN). He was admitted to our hospital with fever, general weakness, arthritis, and purpura. Five weeks after admission, hypertension was noted. Skin biopsy showed perivascular leukocyte infiltration in the epidermis. An aortography revealed multiple aneurysms of the renal, common hepatic, and intercostal arteries. He was treated with intravenous methylprednisolone, oral cyclophosphamide, and azathioprine. The known rare association of FMF and PAN is discussed.
引用
收藏
页码:631 / 633
页数:3
相关论文
共 12 条
[1]  
COHEN RD, 1980, MAYO CLIN PROC, V55, P146
[2]  
CONN DL, 1993, TXB RHEUMATOLOGY, P1077
[3]  
FINK CW, 1986, PEDIATR CLIN N AM, V33, P1203
[4]   SCHONLEIN-HENOCH SYNDROME IN PATIENTS WITH FAMILIAL MEDITERRANEAN FEVER [J].
FLATAU, E ;
KOHN, D ;
SCHILLER, D ;
LURIE, M ;
LEVY, E .
ARTHRITIS AND RHEUMATISM, 1982, 25 (01) :42-47
[5]  
GLIKSON M, 1989, J RHEUMATOL, V16, P536
[6]   DIAGNOSTIC-CRITERIA FOR POLYARTERITIS-NODOSA IN CHILDHOOD [J].
OZEN, S ;
BESBAS, N ;
SAATCI, U ;
BAKKALOGLU, A .
JOURNAL OF PEDIATRICS, 1992, 120 (02) :206-209
[7]   FAMILIAL MEDITERRANEAN FEVER AND POLYARTERITIS-NODOSA [J].
OZEN, S ;
SAATCI, U ;
BALKANCI, F ;
BESBAS, N ;
BAKKALOGLU, A ;
TACAL, T .
SCANDINAVIAN JOURNAL OF RHEUMATOLOGY, 1992, 21 (06) :312-313
[8]  
Pras M, 1984, Adv Nephrol Necker Hosp, V13, P261
[9]   SPECTRUM OF RENAL INVOLVEMENT IN FAMILIAL MEDITERRANEAN FEVER [J].
SAID, R ;
HAMZEH, Y ;
SAID, S ;
TARAWNEH, M ;
ALKHATEEB, M .
KIDNEY INTERNATIONAL, 1992, 41 (02) :414-419
[10]   UNUSUAL IMMUNOLOGICAL FINDINGS IN FAMILIAL MEDITERRANEAN FEVER [J].
SAVI, M ;
ASINARI, G ;
GAUDIANO, V ;
OLIVETTI, G ;
NERI, TM .
ARCHIVES OF INTERNAL MEDICINE, 1978, 138 (04) :644-645