Surgical treatment of congenital adrenal hyperplasia

被引：40

作者：

Schnitzer, JJ

Donahoe, PK

机构：

[1] Massachusetts Gen Hosp, Pediat Surg Serv, Boston, MA 02114 USA

[2] Massachusetts Gen Hosp, Pediat Surg Res Lab, Boston, MA 02114 USA

[3] Harvard Univ, Sch Med, Dept Surg, Boston, MA 02115 USA

来源：

ENDOCRINOLOGY AND METABOLISM CLINICS OF NORTH AMERICA | 2001年 / 30卷 / 01期

关键词：

D O I：

10.1016/S0889-8529(08)70023-9

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

This article discusses congenital adrenal hyperplasia (CAH) in the context of normal sex determination and differentiation. Topics include how CAH can be differentiated from other causes of ambiguous genitalia that can produce similar phenotypes, how a rapid diagnosis can be made and early treatment employed to avoid adrenal crisis, the timing of surgery after the child stabilizes, the optimization and use of early surgical correction, and follow-up for anticipated problems that may manifest at adolescence.

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页码：137 / +

页数：20

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