Congenital pulmonary lymphangiectasia: A case report of thoracic duct agenesis

被引：5

作者：

Antonetti, M

Manuck, TA

Schramm, C

Hight, D

机构：

[1] Univ Connecticut, Sch Med, Connecticut Childrens Med Ctr, Dept Pediat Surg & Urol, Hartford, CT 06106 USA

[2] Univ Connecticut, Sch Med, Connecticut Childrens Med Ctr, Dept Pulm Med, Farmington, CT USA

来源：

PEDIATRIC PULMONOLOGY | 2001年 / 32卷 / 02期

关键词：

congenital pulmonary lymphangiectasia; thoracic duct abnormalities; chylothorax;

D O I：

10.1002/ppul.1106.abs

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

We present a 17-year-old Caucasian male with congenital pulmonary lymphangiectasia and an absent thoracic duct. This patient is unique as he did not present with the disorder until age 9.5 years. Since his initial presentation he has had recurrent chylothoraces and has been treated symptomatically. We discuss the possible implications of his disorder as well as some of the limited treatment that is available. (C) 2001 Wiley-Liss, Inc.

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收藏

页码：184 / 186

页数：3

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