Two enlarged kidneys:: A manifestation of Erdheim-Chester disease

被引：23

作者：

André, M

Delèvaux, I

de Fraissinette, B

Ponsonnaille, J

Chalret, NC

Wechsler, B

Piette, JC

Aumaître, O

机构：

[1] Grp Hosp St Jacques, Serv Med Interne, Dept Internal Med, F-63003 Clermont Ferrand 1, France

[2] Grp Hosp St Jacques, Dept Radiol, F-63003 Clermont Ferrand, France

[3] Grp Hosp St Jacques, Dept Pathol, F-63003 Clermont Ferrand 1, France

[4] Grp Hosp St Jacques, Dept Cardiol, F-63003 Clermont Ferrand 1, France

[5] Hop La Pitie Salpetriere, Dept Internal Med, Paris, France

来源：

AMERICAN JOURNAL OF NEPHROLOGY | 2001年 / 21卷 / 04期

关键词：

pericarditis; Erdheim-Chester disease; kidney; enlarged; histiocytosis; computed tomography;

D O I：

10.1159/000046267

中图分类号：

R5 [内科学]; R69 [泌尿科学（泌尿生殖系疾病）];

学科分类号：

1002 ; 100201 ;

摘要：

Erdheim-Chester disease is a rare form of non-Langerhans' cell histiocytosis. This disorder is characterized by a bone involvement and several extraskeletal manifestations. We describe the case of a patient with a pleural and pericardial effusion leading to tamponade. Pathological examination of pericardium and mediastinal adenopathy was normal. The abdominal computed tomography scan showed two enlarged kidneys suggestive of Erdheim-Chester disease. Bone scan scintigraphy demonstrated symmetrical increased labeling of the long bones. The biopsy of perirenal soft tissue confirmed the diagnosis of Erdheim-Chester disease. Copyright (C) 2001 S. Karger AG, Basel.

引用

页码：315 / 317

页数：3

共 5 条

[1] Erdheim-Chester disease - Clinical, radiologic, and histopathologic findings in five patients with interstitial lung disease [J].