Coronary artery patency following long-term successful engraftment 14 years after bone marrow transplantation in the Hurler syndrome

被引:34
作者
Braunlin, EA
Rose, AG
Hopwood, JJ
Candel, RD
Krivit, W
机构
[1] Univ Minnesota, Sch Med, Dept Pediat, Minneapolis, MN 55455 USA
[2] Univ Minnesota, Sch Med, Dept Pathol, Minneapolis, MN 55455 USA
[3] Womens & Childrens Hosp, Adelaide, SA, Australia
[4] N Shore Reg Med Ctr, Slidell, LA USA
关键词
D O I
10.1016/S0002-9149(01)01999-3
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
The coronary arteries in a patient with the Hurler Syndrome appear only minimally affected by the deposition of glycosaminoglycans 14 years after successful bone marrow engraftment. This finding is added to the previously reported salutary effects of transplant on large airways, cardiac function, hepatic morphology, and central nervous system function.
引用
收藏
页码:1075 / +
页数:4
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