Malignant hypertension and cerebral haemorrhage in Seckel syndrome

被引:22
作者
Di Bartolomeo, R
Polidori, G
Piastra, M
Viola, L
Zampino, G
Chiaretti, A
机构
[1] Policlin A Gemelli, Inst Paediat, I-00168 Rome, Italy
[2] Catholic Univ Med Sch Rome, Paediat Intens Care Unit, Rome, Italy
关键词
aneurysm; cerebral haemorrhage; malignant hypertension; Seckel syndrome;
D O I
10.1007/s00431-003-1310-z
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Seckel syndrome is an autosomal recessive condition with severe short stature and facial and neurological anomalies. Intracranial haemorrhage, due to rupture of a cerebral aneurysm, is a very rare complication of this syndrome. Malignant hypertension may play an important role in the aetiology of the aneurysm and early detection is essential in order to prevent organ damage. Conclusion:we report a new case of Seckel syndrome associated with malignant hypertension and cerebral haemorrhage.
引用
收藏
页码:860 / 862
页数:3
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