Megakaryocytes derived from patients with the classical form of Bernard-Soulier syndrome show no ability to extend proplatelets in vitro

被引:24
作者
Balduini, Alessandra [1 ]
Malara, Alessandro [1 ]
Balduini, Carlo L. [2 ]
Noris, Patrizia [2 ]
机构
[1] Univ Pavia, Dept Biochem, IRCCS Policlin San Matteo Fdn, I-27100 Pavia, Italy
[2] Univ Pavia, Dept Internal Med, IRCCS Policlin San Matteo Fdn, I-27100 Pavia, Italy
关键词
Bernard-Soulier syndrome; megakarypoiesis; proplatelet formation; MACROTHROMBOCYTOPENIA; THROMBOCYTOPENIA; PLATELETS; MODEL;
D O I
10.3109/09537104.2010.547960
中图分类号
Q2 [细胞生物学];
学科分类号
071009 ; 090102 ;
摘要
引用
收藏
页码:308 / 311
页数:4
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