Cellular defenses against unfolded proteins: A cell biologist thinks about neurodegenerative diseases

被引:817
作者
Sherman, MY
Goldberg, AL
机构
[1] Boston Biomed Res Inst, Watertown, MA 02472 USA
[2] Harvard Univ, Sch Med, Dept Cell Biol, Boston, MA 02115 USA
关键词
D O I
10.1016/S0896-6273(01)00177-5
中图分类号
Q189 [神经科学];
学科分类号
071006 ;
摘要
[No abstract available]
引用
收藏
页码:15 / 32
页数:18
相关论文
共 192 条
  • [1] AMRANI M, 1993, CARDIOSCIENCE, V4, P193
  • [2] ABNORMAL PROTEINS SERVE AS EUKARYOTIC STRESS SIGNALS AND TRIGGER THE ACTIVATION OF HEAT-SHOCK GENES
    ANANTHAN, J
    GOLDBERG, AL
    VOELLMY, R
    [J]. SCIENCE, 1986, 232 (4749) : 522 - 524
  • [3] Intracellular localization of proteasomal degradation of a viral antigen
    Antón, LC
    Schubert, U
    Bacík, I
    Princiotta, MF
    Wearsch, PA
    Gibbs, J
    Day, PM
    Realini, C
    Rechsteiner, MC
    Bennink, JR
    Yewdell, JW
    [J]. JOURNAL OF CELL BIOLOGY, 1999, 146 (01) : 113 - 124
  • [4] CAG EXPANSION AFFECTS THE EXPRESSION OF MUTANT HUNTINGTIN IN THE HUNTINGTONS-DISEASE BRAIN
    ARONIN, N
    CHASE, K
    YOUNG, C
    SAPP, E
    SCHWARZ, C
    MATTA, N
    KORNREICH, R
    LANDWEHRMEYER, B
    BIRD, E
    BEAL, MF
    VONSATTEL, JP
    SMITH, T
    CARRAWAY, R
    BOYCE, FM
    YOUNG, AB
    PENNEY, JB
    DIFIGLIA, M
    [J]. NEURON, 1995, 15 (05) : 1193 - 1201
  • [5] DENATURED HEMOGLOBIN IN SICKLE ERYTHROCYTES
    ASAKURA, T
    MINAKATA, K
    ADACHI, K
    RUSSELL, MO
    SCHWARTZ, E
    [J]. JOURNAL OF CLINICAL INVESTIGATION, 1977, 59 (04) : 633 - 640
  • [6] Baba M, 1998, AM J PATHOL, V152, P879
  • [7] Baler R, 1996, CELL STRESS CHAPERON, V1, P33, DOI 10.1379/1466-1268(1996)001<0033:EFAROH>2.3.CO
  • [8] 2
  • [9] Expansion of polyglutamine repeat in huntingtin leads to abnormal protein interactions involving calmodulin
    Bao, J
    Sharp, AH
    Wagster, MV
    Becher, M
    Schilling, G
    Ross, CA
    Dawson, VL
    Dawson, TM
    [J]. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1996, 93 (10) : 5037 - 5042
  • [10] Transgenic mice in the study of polyglutamine repeat expansion diseases
    Bates, GP
    Mangiarini, L
    Davies, SW
    [J]. BRAIN PATHOLOGY, 1998, 8 (04) : 699 - 714