Neurodegeneration: Of (transgenic) mice and men

被引:6
作者
Aguzzi, A [1 ]
Raeber, AJ [1 ]
机构
[1] Univ Zurich Hosp, Dept Pathol, Inst Neuropathol, CH-8091 Zurich, Switzerland
关键词
D O I
10.1111/j.1750-3639.1998.tb00195.x
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
引用
收藏
页码:695 / 697
页数:3
相关论文
共 16 条
[1]   Transgenic mice in the study of polyglutamine repeat expansion diseases [J].
Bates, GP ;
Mangiarini, L ;
Davies, SW .
BRAIN PATHOLOGY, 1998, 8 (04) :699-714
[2]   Transgenic mouse models of Alzheimer's disease and amyotrophic lateral sclerosis [J].
Borchelt, DR ;
Wong, PC ;
Sisodia, SS ;
Price, DL .
BRAIN PATHOLOGY, 1998, 8 (04) :735-757
[3]   RESISTANCE OF SCRAPIE INFECTIVITY TO STEAM AUTOCLAVING AFTER FORMALDEHYDE FIXATION AND LIMITED SURVIVAL AFTER ASHING AT 360-DEGREES-C - PRACTICAL AND THEORETICAL IMPLICATIONS [J].
BROWN, P ;
LIBERSKI, PP ;
WOLFF, A ;
GAJDUSEK, DC .
JOURNAL OF INFECTIOUS DISEASES, 1990, 161 (03) :467-472
[4]   Are neuronal intranuclear inclusions the common neuropathology of triplet-repeat disorders with polyglutamine-repeat expansions? [J].
Davies, SW ;
Beardsall, K ;
Turmaine, M ;
DiFiglia, M ;
Aronin, N ;
Bates, GP .
LANCET, 1998, 351 (9096) :131-133
[5]   The lurcher mutation and ionotropic glutamate receptors:: Contributions to programmed neuronal death in vivo [J].
De Jager, PL ;
Heintz, N .
BRAIN PATHOLOGY, 1998, 8 (04) :795-807
[6]   Transgenic mice in the study of ALS:: The role of neurofilaments [J].
Julien, JP ;
Couillard-Després, S ;
Meier, J .
BRAIN PATHOLOGY, 1998, 8 (04) :759-769
[7]   MECHANISM OF SCRAPIE REPLICATION [J].
LANSBURY, PT .
SCIENCE, 1994, 265 (5178) :1510-1510
[8]   A NOVEL GENE CONTAINING A TRINUCLEOTIDE REPEAT THAT IS EXPANDED AND UNSTABLE ON HUNTINGTONS-DISEASE CHROMOSOMES [J].
MACDONALD, ME ;
AMBROSE, CM ;
DUYAO, MP ;
MYERS, RH ;
LIN, C ;
SRINIDHI, L ;
BARNES, G ;
TAYLOR, SA ;
JAMES, M ;
GROOT, N ;
MACFARLANE, H ;
JENKINS, B ;
ANDERSON, MA ;
WEXLER, NS ;
GUSELLA, JF ;
BATES, GP ;
BAXENDALE, S ;
HUMMERICH, H ;
KIRBY, S ;
NORTH, M ;
YOUNGMAN, S ;
MOTT, R ;
ZEHETNER, G ;
SEDLACEK, Z ;
POUSTKA, A ;
FRISCHAUF, AM ;
LEHRACH, H ;
BUCKLER, AJ ;
CHURCH, D ;
DOUCETTESTAMM, L ;
ODONOVAN, MC ;
RIBARAMIREZ, L ;
SHAH, M ;
STANTON, VP ;
STROBEL, SA ;
DRATHS, KM ;
WALES, JL ;
DERVAN, P ;
HOUSMAN, DE ;
ALTHERR, M ;
SHIANG, R ;
THOMPSON, L ;
FIELDER, T ;
WASMUTH, JJ ;
TAGLE, D ;
VALDES, J ;
ELMER, L ;
ALLARD, M ;
CASTILLA, L ;
SWAROOP, M .
CELL, 1993, 72 (06) :971-983
[9]   Exon 1 of the HD gene with an expanded CAG repeat is sufficient to cause a progressive neurological phenotype in transgenic mice [J].
Mangiarini, L ;
Sathasivam, K ;
Seller, M ;
Cozens, B ;
Harper, A ;
Hetherington, C ;
Lawton, M ;
Trottier, Y ;
Lehrach, H ;
Davies, SW ;
Bates, GP .
CELL, 1996, 87 (03) :493-506
[10]   Prion diseases and the BSE crisis [J].
Prusiner, SB .
SCIENCE, 1997, 278 (5336) :245-251