Peripheral T cell lymphoma in a patient with common variable immunodeficiency disease: Case report and literature review

被引:24
作者
Gottesman, SRS [1 ]
Haas, D [1 ]
Ladanyi, M [1 ]
Amorosi, EL [1 ]
机构
[1] SUNY Hlth Sci Ctr, Dept Pathol, Brooklyn, NY 11203 USA
关键词
peripheral T-cell lymphoma; common variable immunodeficiency disease; EBV; T-cell receptor gene rearrangement;
D O I
10.3109/10428199909058418
中图分类号
R73 [肿瘤学];
学科分类号
100214 ;
摘要
This report documents the occurrence of a peripheral T cell lymphoma arising in the bone marrow and liver of a patient with common variable immunodeficiency disease. The T cell origin of this lymphoma was demonstrated by immunohistochemical phenotyping and gene rearrangement studies and was not associated with EBV infection of the lymphoma cells. The frequency and characteristics of lymphomas complicating CVID are reviewed.
引用
收藏
页码:589 / 595
页数:7
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