Factor H-US?

被引:13
作者
Warwicker, P
Goodship, JA
Goodship, THJ
机构
[1] Lister Hosp, Renal Unit, Stevenage SG1 4AB, Herts, England
[2] Univ Newcastle Upon Tyne, Dept Med, Newcastle Upon Tyne NE1 7RU, Tyne & Wear, England
[3] Univ Newcastle Upon Tyne, Dept Human Genet, Newcastle Upon Tyne NE1 7RU, Tyne & Wear, England
关键词
D O I
10.1093/ndt/13.8.1921
中图分类号
R3 [基础医学]; R4 [临床医学];
学科分类号
1001 ; 1002 ; 100602 ;
摘要
引用
收藏
页码:1921 / 1923
页数:3
相关论文
共 39 条
[1]   Human factor H deficiency - Mutations in framework cysteine residues and block in H protein secretion and intracellular catabolism [J].
Ault, BH ;
Schmidt, BZ ;
Fowler, NL ;
Kashtan, CE ;
Ahmed, AE ;
Vogt, BA ;
Colten, HR .
JOURNAL OF BIOLOGICAL CHEMISTRY, 1997, 272 (40) :25168-25175
[2]   IMPROVED SURVIVAL IN THROMBOTIC THROMBOCYTOPENIC PURPURA HEMOLYTIC UREMIC SYNDROME - CLINICAL-EXPERIENCE IN 108 PATIENTS [J].
BELL, WR ;
BRAINE, HG ;
NESS, PM ;
KICKLER, TS .
NEW ENGLAND JOURNAL OF MEDICINE, 1991, 325 (06) :398-403
[3]   RECURRENT HEMOLYTIC-UREMIC SYNDROME WITH HYPOCOMPLEMENTEMIA - A CASE-REPORT [J].
BOGDANOVIC, R ;
CVORIC, A ;
NIKOLIC, V ;
SINDJIC, M .
PEDIATRIC NEPHROLOGY, 1988, 2 (02) :236-238
[4]   COMBINED HOMOZYGOUS FACTOR-H AND HETEROZYGOUS C2 DEFICIENCY IN AN ITALIAN FAMILY [J].
BRAI, M ;
MISIANO, G ;
MARINGHINI, S ;
CUTAJA, I ;
HAUPTMANN, G .
JOURNAL OF CLINICAL IMMUNOLOGY, 1988, 8 (01) :50-56
[5]  
CAMERON JS, 1973, LANCET, V2, P975
[6]   FAMILIAL HYPOCOMPLEMENTEMIC HEMOLYTIC UREMIC SYNDROME WITH HLA-A3,B7-HAPLOTYPE [J].
CARRERAS, L ;
ROMERO, R ;
REQUESENS, C ;
OLIVER, AJ ;
CARRERA, M ;
CLAVO, M ;
ALSINA, J .
JAMA-JOURNAL OF THE AMERICAN MEDICAL ASSOCIATION, 1981, 245 (06) :602-604
[7]  
FARR MJ, 1975, Q J MED, V44, P161
[8]  
FIJEN CAP, 1992, IMMUNOBIOLOGY, V184, P427
[9]  
HAMMAR SP, 1978, AM J CLIN PATHOL, V70, P434
[10]  
HOGASEN K, 1997, J AM SOC NEPHROL, V8, pA474