Relationship of the Tufts Quantitative Neuromuscular Exam (TQNE) and the Sickness Impact Profile (SIP) in measuring progression of ALS

被引:51
作者
McGuire, D
Garrison, L
Armon, C
Barohn, R
Bryan, W
Miller, R
Parry, G
Petajan, J
Ross, M
Alternus, P
Amox, D
Ashburn, C
Aulenbacher, D
Blasucci, L
Brown, E
Caulkins, M
Carozza, C
Dao, H
Davis, L
Driscoll, T
Frierson, L
Fuqua, P
Gardner, H
Golbesky, B
Good, B
Graves, J
Harstock, L
Hawkins, C
Hernandez, R
Iturriaga, E
Kres, J
Laurenzi, B
Lee, E
Leyde, D
Mehagian, M
Moses, D
Nash, J
Norwood, N
Parsons, J
Pearmain, J
RatliffWalker, D
Rightmyer, D
Rizzi, V
Smith, B
Soliman, M
Volintine, L
Warder, J
Werner, J
Wolf, S
机构
[1] LOMA LINDA UNIV,MED CTR,DEPT NEUROL,LOMA LINDA,CA
[2] UNIV TEXAS,SW MED SCH,DEPT NEUROL,DALLAS,TX
[3] CALIF PACIFIC MED CTR,DEPT NEUROL,SAN FRANCISCO,CA
[4] UNIV MINNESOTA,DEPT NEUROL,MINNEAPOLIS,MN 55455
[5] UNIV UTAH,DEPT NEUROL,SALT LAKE CITY,UT 84112
[6] UNIV IOWA HOSP & CLIN,DEPT NEUROL,IOWA CITY,IA 52242
关键词
D O I
10.1212/WNL.46.5.1442
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
The Tufts Quantitative Neuromuscular Exam (TQNE) is a standardized tool for measuring muscle strength and pulmonary function in patients with amyotrophic lateral sclerosis (ALS). We describe the relationship of TQNE scores to functional disability and health-related quality of life as measured by the Sickness Impact Profile (SIP) in 524 ALS patients. There was a significant relationship (p < 0.0001) between TQNE and SIP scores, both in cross section and over time. TQNE scores strongly relate to ALS patients' quality of life and ability to perform activities of daily living.
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页码:1442 / 1444
页数:3
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