共 9 条
Is Upshaw-Schulman syndrome congenital thrombotic thrombocytopenic purpura or hemolytic-uremic syndrome? Yes to both
被引:4
作者:

Fujimura, Y
论文数: 0 引用数: 0
h-index: 0
机构:
Nara Med Univ, Dept Blood Transfus Med, Kashihara, Nara 6348522, Japan Nara Med Univ, Dept Blood Transfus Med, Kashihara, Nara 6348522, Japan
机构:
[1] Nara Med Univ, Dept Blood Transfus Med, Kashihara, Nara 6348522, Japan
关键词:
D O I:
10.1046/j.1538-7836.2003.0468f.x
中图分类号:
R5 [内科学];
学科分类号:
1002 ;
100201 ;
摘要:
引用
收藏
页码:2457 / 2458
页数:2
相关论文
共 9 条
[1]
Von Willebrand factor-cleaving protease in thrombotic thrombocytopenic purpura and the hemolytic-uremic syndrome
[J].
Furlan, M
;
Robles, R
;
Galbusera, M
;
Remuzzi, G
;
Kyrle, PA
;
Brenner, B
;
Krause, M
;
Scharrer, I
;
Aumann, V
;
Mittler, U
;
Solenthaler, M
;
Lämmle, B
.
NEW ENGLAND JOURNAL OF MEDICINE,
1998, 339 (22)
:1578-1584

Furlan, M
论文数: 0 引用数: 0
h-index: 0
机构:
Univ Hosp Bern, Inselspital, Cent Hematol Lab, CH-3010 Bern, Switzerland Univ Hosp Bern, Inselspital, Cent Hematol Lab, CH-3010 Bern, Switzerland

Robles, R
论文数: 0 引用数: 0
h-index: 0
机构: Univ Hosp Bern, Inselspital, Cent Hematol Lab, CH-3010 Bern, Switzerland

Galbusera, M
论文数: 0 引用数: 0
h-index: 0
机构: Univ Hosp Bern, Inselspital, Cent Hematol Lab, CH-3010 Bern, Switzerland

Remuzzi, G
论文数: 0 引用数: 0
h-index: 0
机构: Univ Hosp Bern, Inselspital, Cent Hematol Lab, CH-3010 Bern, Switzerland

Kyrle, PA
论文数: 0 引用数: 0
h-index: 0
机构: Univ Hosp Bern, Inselspital, Cent Hematol Lab, CH-3010 Bern, Switzerland

Brenner, B
论文数: 0 引用数: 0
h-index: 0
机构: Univ Hosp Bern, Inselspital, Cent Hematol Lab, CH-3010 Bern, Switzerland

Krause, M
论文数: 0 引用数: 0
h-index: 0
机构: Univ Hosp Bern, Inselspital, Cent Hematol Lab, CH-3010 Bern, Switzerland

Scharrer, I
论文数: 0 引用数: 0
h-index: 0
机构: Univ Hosp Bern, Inselspital, Cent Hematol Lab, CH-3010 Bern, Switzerland

Aumann, V
论文数: 0 引用数: 0
h-index: 0
机构: Univ Hosp Bern, Inselspital, Cent Hematol Lab, CH-3010 Bern, Switzerland

Mittler, U
论文数: 0 引用数: 0
h-index: 0
机构: Univ Hosp Bern, Inselspital, Cent Hematol Lab, CH-3010 Bern, Switzerland

Solenthaler, M
论文数: 0 引用数: 0
h-index: 0
机构: Univ Hosp Bern, Inselspital, Cent Hematol Lab, CH-3010 Bern, Switzerland

Lämmle, B
论文数: 0 引用数: 0
h-index: 0
机构: Univ Hosp Bern, Inselspital, Cent Hematol Lab, CH-3010 Bern, Switzerland
[2]
Mutations and common polymorphisms in ADAMTS13 gene responsiblefor von Willebrand factor-cleaving protease activity
[J].
Kokame, K
;
Matsumoto, M
;
Soejima, K
;
Yagi, H
;
Ishizashi, H
;
Funato, M
;
Tamai, H
;
Konno, M
;
Kamide, K
;
Kawano, Y
;
Miyata, T
;
Fujimura, Y
.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA,
2002, 99 (18)
:11902-11907

Kokame, K
论文数: 0 引用数: 0
h-index: 0
机构: Natl Cardiovasc Ctr, Res Inst, Suita, Osaka 5658565, Japan

Matsumoto, M
论文数: 0 引用数: 0
h-index: 0
机构: Natl Cardiovasc Ctr, Res Inst, Suita, Osaka 5658565, Japan

Soejima, K
论文数: 0 引用数: 0
h-index: 0
机构: Natl Cardiovasc Ctr, Res Inst, Suita, Osaka 5658565, Japan

Yagi, H
论文数: 0 引用数: 0
h-index: 0
机构: Natl Cardiovasc Ctr, Res Inst, Suita, Osaka 5658565, Japan

Ishizashi, H
论文数: 0 引用数: 0
h-index: 0
机构: Natl Cardiovasc Ctr, Res Inst, Suita, Osaka 5658565, Japan

Funato, M
论文数: 0 引用数: 0
h-index: 0
机构: Natl Cardiovasc Ctr, Res Inst, Suita, Osaka 5658565, Japan

Tamai, H
论文数: 0 引用数: 0
h-index: 0
机构: Natl Cardiovasc Ctr, Res Inst, Suita, Osaka 5658565, Japan

Konno, M
论文数: 0 引用数: 0
h-index: 0
机构: Natl Cardiovasc Ctr, Res Inst, Suita, Osaka 5658565, Japan

Kamide, K
论文数: 0 引用数: 0
h-index: 0
机构: Natl Cardiovasc Ctr, Res Inst, Suita, Osaka 5658565, Japan

Kawano, Y
论文数: 0 引用数: 0
h-index: 0
机构: Natl Cardiovasc Ctr, Res Inst, Suita, Osaka 5658565, Japan

Miyata, T
论文数: 0 引用数: 0
h-index: 0
机构:
Natl Cardiovasc Ctr, Res Inst, Suita, Osaka 5658565, Japan Natl Cardiovasc Ctr, Res Inst, Suita, Osaka 5658565, Japan

Fujimura, Y
论文数: 0 引用数: 0
h-index: 0
机构: Natl Cardiovasc Ctr, Res Inst, Suita, Osaka 5658565, Japan
[3]
Clustering of missense mutations in the C-terminal region of factor H in atypical hemolytic uremic syndrome
[J].
Pérez-Caballero, D
;
González-Rubio, C
;
Gallardo, ME
;
Vera, M
;
López-Trascasa, M
;
de Córdoba, SR
;
Sánchez-Corral, P
.
AMERICAN JOURNAL OF HUMAN GENETICS,
2001, 68 (02)
:478-484

Pérez-Caballero, D
论文数: 0 引用数: 0
h-index: 0
机构: CSIC, Ctr Invest Biol, Dept Inmunol, E-28006 Madrid, Spain

González-Rubio, C
论文数: 0 引用数: 0
h-index: 0
机构: CSIC, Ctr Invest Biol, Dept Inmunol, E-28006 Madrid, Spain

Gallardo, ME
论文数: 0 引用数: 0
h-index: 0
机构: CSIC, Ctr Invest Biol, Dept Inmunol, E-28006 Madrid, Spain

Vera, M
论文数: 0 引用数: 0
h-index: 0
机构: CSIC, Ctr Invest Biol, Dept Inmunol, E-28006 Madrid, Spain

López-Trascasa, M
论文数: 0 引用数: 0
h-index: 0
机构: CSIC, Ctr Invest Biol, Dept Inmunol, E-28006 Madrid, Spain

de Córdoba, SR
论文数: 0 引用数: 0
h-index: 0
机构: CSIC, Ctr Invest Biol, Dept Inmunol, E-28006 Madrid, Spain

Sánchez-Corral, P
论文数: 0 引用数: 0
h-index: 0
机构: CSIC, Ctr Invest Biol, Dept Inmunol, E-28006 Madrid, Spain
[4]
Is ADAMTS-13 deficiency specific for thrombotic thrombocytopenic purpura? No
[J].
Remuzzi, G
.
JOURNAL OF THROMBOSIS AND HAEMOSTASIS,
2003, 1 (04)
:632-634

Remuzzi, G
论文数: 0 引用数: 0
h-index: 0
机构: Mario Negri Inst Pharmacol Res, Negri Bergamo Labs, I-24125 Bergamo, Italy
[5]
von Willebrand factor cleaving protease (ADAMTS13) is deficient in recurrent and familial thrombotic thrombocytopenic purpura and hemolytic uremic syndrome
[J].
Remuzzi, G
;
Galbusera, M
;
Noris, M
;
Canciani, MT
;
Daina, E
;
Bresin, E
;
Contaretti, S
;
Caprioli, J
;
Gamba, S
;
Ruggenenti, P
;
Perico, N
;
Mannucci, PM
.
BLOOD,
2002, 100 (03)
:778-785

论文数: 引用数:
h-index:
机构:

论文数: 引用数:
h-index:
机构:

Noris, M
论文数: 0 引用数: 0
h-index: 0
机构: Univ Milan, Milan, Italy

Canciani, MT
论文数: 0 引用数: 0
h-index: 0
机构: Univ Milan, Milan, Italy

Daina, E
论文数: 0 引用数: 0
h-index: 0
机构: Univ Milan, Milan, Italy

Bresin, E
论文数: 0 引用数: 0
h-index: 0
机构: Univ Milan, Milan, Italy

Contaretti, S
论文数: 0 引用数: 0
h-index: 0
机构: Univ Milan, Milan, Italy

Caprioli, J
论文数: 0 引用数: 0
h-index: 0
机构: Univ Milan, Milan, Italy

Gamba, S
论文数: 0 引用数: 0
h-index: 0
机构: Univ Milan, Milan, Italy

Ruggenenti, P
论文数: 0 引用数: 0
h-index: 0
机构: Univ Milan, Milan, Italy

论文数: 引用数:
h-index:
机构:

论文数: 引用数:
h-index:
机构:
[6]
STUDIES ON THROMBOPOESIS .1. A FACTOR IN NORMAL HUMAN PLASMA REQUIRED FOR PLATELET PRODUCTION - CHRONIC THROMBOCYTOPENIA DUE TO ITS DEFICIENCY
[J].
SCHULMAN, I
;
PIERCE, M
;
LUKENS, A
;
CURRIMBHOY, Z
.
BLOOD,
1960, 16 (01)
:943-957

SCHULMAN, I
论文数: 0 引用数: 0
h-index: 0

PIERCE, M
论文数: 0 引用数: 0
h-index: 0

LUKENS, A
论文数: 0 引用数: 0
h-index: 0

CURRIMBHOY, Z
论文数: 0 引用数: 0
h-index: 0
[7]
Is severe deficiency of ADAMTS-13 specific for thrombotic thrombocytopenic purpura? Yes
[J].
Tsai, HM
.
JOURNAL OF THROMBOSIS AND HAEMOSTASIS,
2003, 1 (04)
:625-631

Tsai, HM
论文数: 0 引用数: 0
h-index: 0
机构: Montefiore Med Ctr, Div Hematol, Bronx, NY 10467 USA
[8]
Antibodies to von Willebrand factor-cleaving protease in acute thrombotic thrombocytopenic purpura
[J].
Tsai, HM
;
Lian, ECY
.
NEW ENGLAND JOURNAL OF MEDICINE,
1998, 339 (22)
:1585-1594

Tsai, HM
论文数: 0 引用数: 0
h-index: 0
机构: Montefiore Med Ctr, Div Hematol, Bronx, NY 10467 USA

Lian, ECY
论文数: 0 引用数: 0
h-index: 0
机构: Montefiore Med Ctr, Div Hematol, Bronx, NY 10467 USA
[9]
CONGENITAL DEFICIENCY OF A FACTOR IN NORMAL PLASMA THAT REVERSES MICRO-ANGIOPATHIC HEMOLYSIS AND THROMBOCYTOPENIA
[J].
UPSHAW, JD
.
NEW ENGLAND JOURNAL OF MEDICINE,
1978, 298 (24)
:1350-1352

UPSHAW, JD
论文数: 0 引用数: 0
h-index: 0