Spontaneous aortic dissection and rupture in a patient with neurofibromatosis

被引:31
作者
Chew, DKW
Muto, PM
Gordon, JK
Straceski, AJ
Donaldson, MC
机构
[1] Harvard Univ, Sch Med, Brigham & Womens Hosp, Div Vasc Surg, Boston, MA 02115 USA
[2] Lawrence Gen Hosp, Dept Surg, Lawrence, MA USA
[3] Lawrence Gen Hosp, Dept Med, Lawrence, MA USA
关键词
D O I
10.1067/mva.2001.116141
中图分类号
R61 [外科手术学];
学科分类号
摘要
Vascular involvement in neurofibromatosis type I is a well-recognized but rare feature of the disease. This case report is the first such describing acute aortic dissection and rupture in a patient who also had incidental aneurysms of his carotid and iliac arteries. A review of the literature about pathogenesis and management strategies is also presented.
引用
收藏
页码:364 / 366
页数:3
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