Congo red, doxycycline, and HSP70 overexpression reduce aggregate formation and cell death in cell models of oculopharyngeal muscular dystrophy

被引:41
作者
Bao, YP
Sarkar, S
Uyama, E
Rubinsztein, DC
机构
[1] Addenbrookes Hosp, Cambridge Inst Med Res, Dept Med Genet, Cambridge CB2 2XY, England
[2] Kumamoto Univ, Sch Med, Dept Neurol, Kumamoto 8600811, Japan
来源
JOURNAL OF MEDICAL GENETICS | 2004年 / 41卷 / 01期
关键词
D O I
10.1136/jmg.2003.014548
中图分类号
Q3 [遗传学];
学科分类号
071007 ; 090102 ;
摘要
[No abstract available]
引用
收藏
页码:47 / 51
页数:5
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