Arrhythmogenic right ventricular dysplasia cardiomyopathy: Review for the clinician

被引:28
作者
Ananthasubramaniam, K [1 ]
Khaja, F [1 ]
机构
[1] Henry Ford Hosp, Div Cardiol, Cardiac Cath Lab, Inst Heart & Vasc, Detroit, MI 48202 USA
关键词
D O I
10.1016/S0033-0620(98)80058-3
中图分类号
R5 [内科学];
学科分类号
1002 [临床医学]; 100201 [内科学];
摘要
Although hypertrophic obstructive cardiomyopathy remains the most common cause of sudden cardiac death in young people, rarer causes, such as arrhythmogenic right ventricular dysplasia (ARVD), are now being increasingly recognized to lead to sudden cardiac death in the younger population. Recent advances in the understanding of the genetic inheritance, etiopathogenesis, diagnosis, and treatment options of ARVD have prompted a lot of research in this form of right ventricular cardiomyopathy. The purpose of this report is to review the etiopathogenesis, clinical manifestations, diagnosis and treatment modalities for ARVD, and recent advances in the understanding of this disease entity.
引用
收藏
页码:237 / 246
页数:10
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