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Bernard-Soulier syndrome
被引:400
作者
:
López, JA
论文数:
0
引用数:
0
h-index:
0
机构:
Vet Affairs Med Ctr, Houston, TX 77030 USA
López, JA
Andrews, RK
论文数:
0
引用数:
0
h-index:
0
机构:
Vet Affairs Med Ctr, Houston, TX 77030 USA
Andrews, RK
Afshar-Kharghan, V
论文数:
0
引用数:
0
h-index:
0
机构:
Vet Affairs Med Ctr, Houston, TX 77030 USA
Afshar-Kharghan, V
Berndt, MC
论文数:
0
引用数:
0
h-index:
0
机构:
Vet Affairs Med Ctr, Houston, TX 77030 USA
Berndt, MC
机构
:
[1]
Vet Affairs Med Ctr, Houston, TX 77030 USA
[2]
Baker Med Res Inst, Hazel & Pip Appel Vasc Biol Lab, Prahran, Vic 3181, Australia
[3]
Baylor Coll Med, Dept Med, Houston, TX 77030 USA
[4]
Baylor Coll Med, Dept Human Genet, Houston, TX 77030 USA
来源
:
BLOOD
|
1998年
/ 91卷
/ 12期
关键词
:
D O I
:
10.1182/blood.V91.12.4397.412k42_4397_4418
中图分类号
:
R5 [内科学];
学科分类号
:
1002 ;
100201 ;
摘要
:
引用
收藏
页码:4397 / 4418
页数:22
相关论文
共 219 条
[1]
Bernard-Soulier syndrome caused by a dinucleotide deletion and reading frameshift in the region encoding the glycoprotein Ib alpha transmembrane domain
[J].
AfsharKharghan, V
论文数:
0
引用数:
0
h-index:
0
机构:
VET AFFAIRS MED CTR,HOUSTON,TX 77030
AfsharKharghan, V
;
Lopez, JA
论文数:
0
引用数:
0
h-index:
0
机构:
VET AFFAIRS MED CTR,HOUSTON,TX 77030
Lopez, JA
.
BLOOD,
1997,
90
(07)
:2634
-2643
[2]
14-3-3 and its possible role in co-ordinating multiple signalling pathways
[J].
Aitken, A
论文数:
0
引用数:
0
h-index:
0
机构:
Laboratory of Protein Structure, Natl. Inst. for Medical Research, London NW7 1AA, Mill Hill
Aitken, A
.
TRENDS IN CELL BIOLOGY,
1996,
6
(09)
:341
-347
[3]
Binding of a novel 50-kilodalton alboaggregin from Trimeresurus albolabris and related viper venom proteins to the platelet membrane glycoprotein Ib-IX-V complex. Effect on platelet aggregation and glycoprotein Ib-mediated platelet activation
[J].
Andrews, RK
论文数:
0
引用数:
0
h-index:
0
机构:
BAKER MED RES INST, PEPTIDE BIOL LAB, PRAHRAN, VIC 3181, AUSTRALIA
Andrews, RK
;
Kroll, MH
论文数:
0
引用数:
0
h-index:
0
机构:
BAKER MED RES INST, PEPTIDE BIOL LAB, PRAHRAN, VIC 3181, AUSTRALIA
Kroll, MH
;
Ward, CM
论文数:
0
引用数:
0
h-index:
0
机构:
BAKER MED RES INST, PEPTIDE BIOL LAB, PRAHRAN, VIC 3181, AUSTRALIA
Ward, CM
;
Rose, JW
论文数:
0
引用数:
0
h-index:
0
机构:
BAKER MED RES INST, PEPTIDE BIOL LAB, PRAHRAN, VIC 3181, AUSTRALIA
Rose, JW
;
Scarborough, RM
论文数:
0
引用数:
0
h-index:
0
机构:
BAKER MED RES INST, PEPTIDE BIOL LAB, PRAHRAN, VIC 3181, AUSTRALIA
Scarborough, RM
;
Smith, AI
论文数:
0
引用数:
0
h-index:
0
机构:
BAKER MED RES INST, PEPTIDE BIOL LAB, PRAHRAN, VIC 3181, AUSTRALIA
Smith, AI
;
Lopez, JA
论文数:
0
引用数:
0
h-index:
0
机构:
BAKER MED RES INST, PEPTIDE BIOL LAB, PRAHRAN, VIC 3181, AUSTRALIA
Lopez, JA
;
Berndt, MC
论文数:
0
引用数:
0
h-index:
0
机构:
BAKER MED RES INST, PEPTIDE BIOL LAB, PRAHRAN, VIC 3181, AUSTRALIA
Berndt, MC
.
BIOCHEMISTRY,
1996,
35
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CROSS-LINKING OF A MONOMERIC 39/34-KDA DISPASE FRAGMENT OF VONWILLEBRAND-FACTOR (LEU-480/VAL-481-GLY-718) TO THE N-TERMINAL REGION OF THE ALPHA-CHAIN OF MEMBRANE GLYCOPROTEIN-IB ON INTACT PLATELETS WITH BIS(SULFOSUCCINIMIDYL) SUBERATE
[J].
ANDREWS, RK
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV SYDNEY, WESTMEAD CTR, THROMBOSIS & CARDIOVASC DIS RES CTR, DEPT MED, WESTMEAD, NSW 2145, AUSTRALIA
ANDREWS, RK
;
GORMAN, JJ
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV SYDNEY, WESTMEAD CTR, THROMBOSIS & CARDIOVASC DIS RES CTR, DEPT MED, WESTMEAD, NSW 2145, AUSTRALIA
GORMAN, JJ
;
BOOTH, WJ
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV SYDNEY, WESTMEAD CTR, THROMBOSIS & CARDIOVASC DIS RES CTR, DEPT MED, WESTMEAD, NSW 2145, AUSTRALIA
BOOTH, WJ
;
CORINO, GL
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV SYDNEY, WESTMEAD CTR, THROMBOSIS & CARDIOVASC DIS RES CTR, DEPT MED, WESTMEAD, NSW 2145, AUSTRALIA
CORINO, GL
;
CASTALDI, PA
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV SYDNEY, WESTMEAD CTR, THROMBOSIS & CARDIOVASC DIS RES CTR, DEPT MED, WESTMEAD, NSW 2145, AUSTRALIA
CASTALDI, PA
;
BERNDT, MC
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV SYDNEY, WESTMEAD CTR, THROMBOSIS & CARDIOVASC DIS RES CTR, DEPT MED, WESTMEAD, NSW 2145, AUSTRALIA
BERNDT, MC
.
BIOCHEMISTRY,
1989,
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PURIFICATION OF BOTROCETIN FROM BOTHROPS-JARARACA VENOM - ANALYSIS OF THE BOTROCETIN-MEDIATED INTERACTION BETWEEN VONWILLEBRAND-FACTOR AND THE HUMAN-PLATELET MEMBRANE GLYCOPROTEIN-IB-IX COMPLEX
[J].
ANDREWS, RK
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV SYDNEY,WESTMEAD CTR,THROMBOSIS & CARDIOVASC DIS RES CTR,DEPT MED,WESTMEAD,NSW 2145,AUSTRALIA
ANDREWS, RK
;
BOOTH, WJ
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV SYDNEY,WESTMEAD CTR,THROMBOSIS & CARDIOVASC DIS RES CTR,DEPT MED,WESTMEAD,NSW 2145,AUSTRALIA
BOOTH, WJ
;
GORMAN, JJ
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV SYDNEY,WESTMEAD CTR,THROMBOSIS & CARDIOVASC DIS RES CTR,DEPT MED,WESTMEAD,NSW 2145,AUSTRALIA
GORMAN, JJ
;
CASTALDI, PA
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV SYDNEY,WESTMEAD CTR,THROMBOSIS & CARDIOVASC DIS RES CTR,DEPT MED,WESTMEAD,NSW 2145,AUSTRALIA
CASTALDI, PA
;
BERNDT, MC
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV SYDNEY,WESTMEAD CTR,THROMBOSIS & CARDIOVASC DIS RES CTR,DEPT MED,WESTMEAD,NSW 2145,AUSTRALIA
BERNDT, MC
.
BIOCHEMISTRY,
1989,
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Molecular mechanisms of platelet adhesion and activation
[J].
Andrews, RK
论文数:
0
引用数:
0
h-index:
0
机构:
BAKER MED RES INST, HAZEL & PIP APPEL VASC BIOL LAB, PRAHRAN, VIC 3181, AUSTRALIA
Andrews, RK
;
Lopez, JA
论文数:
0
引用数:
0
h-index:
0
机构:
BAKER MED RES INST, HAZEL & PIP APPEL VASC BIOL LAB, PRAHRAN, VIC 3181, AUSTRALIA
Lopez, JA
;
Berndt, MC
论文数:
0
引用数:
0
h-index:
0
机构:
BAKER MED RES INST, HAZEL & PIP APPEL VASC BIOL LAB, PRAHRAN, VIC 3181, AUSTRALIA
Berndt, MC
.
INTERNATIONAL JOURNAL OF BIOCHEMISTRY & CELL BIOLOGY,
1997,
29
(01)
:91
-105
[7]
Binding of purified 14-3-3 ζ signaling protein to discrete amino acid sequences within the cytoplasmic domain of the platelet membrane glycoprotein Ib-IX-V complex
[J].
Andrews, RK
论文数:
0
引用数:
0
h-index:
0
机构:
Baker Med Res Inst, Hazel & Pip Appel Vasc Biol Lab, Prahran, Vic 3181, Australia
Baker Med Res Inst, Hazel & Pip Appel Vasc Biol Lab, Prahran, Vic 3181, Australia
Andrews, RK
;
Harris, SJ
论文数:
0
引用数:
0
h-index:
0
机构:
Baker Med Res Inst, Hazel & Pip Appel Vasc Biol Lab, Prahran, Vic 3181, Australia
Baker Med Res Inst, Hazel & Pip Appel Vasc Biol Lab, Prahran, Vic 3181, Australia
Harris, SJ
;
McNally, T
论文数:
0
引用数:
0
h-index:
0
机构:
Baker Med Res Inst, Hazel & Pip Appel Vasc Biol Lab, Prahran, Vic 3181, Australia
Baker Med Res Inst, Hazel & Pip Appel Vasc Biol Lab, Prahran, Vic 3181, Australia
McNally, T
;
Berndt, MC
论文数:
0
引用数:
0
h-index:
0
机构:
Baker Med Res Inst, Hazel & Pip Appel Vasc Biol Lab, Prahran, Vic 3181, Australia
Baker Med Res Inst, Hazel & Pip Appel Vasc Biol Lab, Prahran, Vic 3181, Australia
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机构:
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TOKYO METROPOLITAN INST MED SCI,DEPT CARDIOVASC RES,BUNKYO KU,TOKYO 113,JAPAN
AKAMATSU, N
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SUZUKI, H
论文数:
0
引用数:
0
h-index:
0
机构:
TOKYO METROPOLITAN INST MED SCI,DEPT CARDIOVASC RES,BUNKYO KU,TOKYO 113,JAPAN
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TOKYO METROPOLITAN INST MED SCI,DEPT CARDIOVASC RES,BUNKYO KU,TOKYO 113,JAPAN
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机构:
VIRGINIA COMMONWEALTH UNIV,MED COLL VIRGINIA,RICHMOND,VA 23298
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共 219 条
[1]
Bernard-Soulier syndrome caused by a dinucleotide deletion and reading frameshift in the region encoding the glycoprotein Ib alpha transmembrane domain
[J].
AfsharKharghan, V
论文数:
0
引用数:
0
h-index:
0
机构:
VET AFFAIRS MED CTR,HOUSTON,TX 77030
AfsharKharghan, V
;
Lopez, JA
论文数:
0
引用数:
0
h-index:
0
机构:
VET AFFAIRS MED CTR,HOUSTON,TX 77030
Lopez, JA
.
BLOOD,
1997,
90
(07)
:2634
-2643
[2]
14-3-3 and its possible role in co-ordinating multiple signalling pathways
[J].
Aitken, A
论文数:
0
引用数:
0
h-index:
0
机构:
Laboratory of Protein Structure, Natl. Inst. for Medical Research, London NW7 1AA, Mill Hill
Aitken, A
.
TRENDS IN CELL BIOLOGY,
1996,
6
(09)
:341
-347
[3]
Binding of a novel 50-kilodalton alboaggregin from Trimeresurus albolabris and related viper venom proteins to the platelet membrane glycoprotein Ib-IX-V complex. Effect on platelet aggregation and glycoprotein Ib-mediated platelet activation
[J].
Andrews, RK
论文数:
0
引用数:
0
h-index:
0
机构:
BAKER MED RES INST, PEPTIDE BIOL LAB, PRAHRAN, VIC 3181, AUSTRALIA
Andrews, RK
;
Kroll, MH
论文数:
0
引用数:
0
h-index:
0
机构:
BAKER MED RES INST, PEPTIDE BIOL LAB, PRAHRAN, VIC 3181, AUSTRALIA
Kroll, MH
;
Ward, CM
论文数:
0
引用数:
0
h-index:
0
机构:
BAKER MED RES INST, PEPTIDE BIOL LAB, PRAHRAN, VIC 3181, AUSTRALIA
Ward, CM
;
Rose, JW
论文数:
0
引用数:
0
h-index:
0
机构:
BAKER MED RES INST, PEPTIDE BIOL LAB, PRAHRAN, VIC 3181, AUSTRALIA
Rose, JW
;
Scarborough, RM
论文数:
0
引用数:
0
h-index:
0
机构:
BAKER MED RES INST, PEPTIDE BIOL LAB, PRAHRAN, VIC 3181, AUSTRALIA
Scarborough, RM
;
Smith, AI
论文数:
0
引用数:
0
h-index:
0
机构:
BAKER MED RES INST, PEPTIDE BIOL LAB, PRAHRAN, VIC 3181, AUSTRALIA
Smith, AI
;
Lopez, JA
论文数:
0
引用数:
0
h-index:
0
机构:
BAKER MED RES INST, PEPTIDE BIOL LAB, PRAHRAN, VIC 3181, AUSTRALIA
Lopez, JA
;
Berndt, MC
论文数:
0
引用数:
0
h-index:
0
机构:
BAKER MED RES INST, PEPTIDE BIOL LAB, PRAHRAN, VIC 3181, AUSTRALIA
Berndt, MC
.
BIOCHEMISTRY,
1996,
35
(38)
:12629
-12639
[4]
CROSS-LINKING OF A MONOMERIC 39/34-KDA DISPASE FRAGMENT OF VONWILLEBRAND-FACTOR (LEU-480/VAL-481-GLY-718) TO THE N-TERMINAL REGION OF THE ALPHA-CHAIN OF MEMBRANE GLYCOPROTEIN-IB ON INTACT PLATELETS WITH BIS(SULFOSUCCINIMIDYL) SUBERATE
[J].
ANDREWS, RK
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV SYDNEY, WESTMEAD CTR, THROMBOSIS & CARDIOVASC DIS RES CTR, DEPT MED, WESTMEAD, NSW 2145, AUSTRALIA
ANDREWS, RK
;
GORMAN, JJ
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV SYDNEY, WESTMEAD CTR, THROMBOSIS & CARDIOVASC DIS RES CTR, DEPT MED, WESTMEAD, NSW 2145, AUSTRALIA
GORMAN, JJ
;
BOOTH, WJ
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV SYDNEY, WESTMEAD CTR, THROMBOSIS & CARDIOVASC DIS RES CTR, DEPT MED, WESTMEAD, NSW 2145, AUSTRALIA
BOOTH, WJ
;
CORINO, GL
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV SYDNEY, WESTMEAD CTR, THROMBOSIS & CARDIOVASC DIS RES CTR, DEPT MED, WESTMEAD, NSW 2145, AUSTRALIA
CORINO, GL
;
CASTALDI, PA
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV SYDNEY, WESTMEAD CTR, THROMBOSIS & CARDIOVASC DIS RES CTR, DEPT MED, WESTMEAD, NSW 2145, AUSTRALIA
CASTALDI, PA
;
BERNDT, MC
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV SYDNEY, WESTMEAD CTR, THROMBOSIS & CARDIOVASC DIS RES CTR, DEPT MED, WESTMEAD, NSW 2145, AUSTRALIA
BERNDT, MC
.
BIOCHEMISTRY,
1989,
28
(21)
:8326
-8336
[5]
PURIFICATION OF BOTROCETIN FROM BOTHROPS-JARARACA VENOM - ANALYSIS OF THE BOTROCETIN-MEDIATED INTERACTION BETWEEN VONWILLEBRAND-FACTOR AND THE HUMAN-PLATELET MEMBRANE GLYCOPROTEIN-IB-IX COMPLEX
[J].
ANDREWS, RK
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV SYDNEY,WESTMEAD CTR,THROMBOSIS & CARDIOVASC DIS RES CTR,DEPT MED,WESTMEAD,NSW 2145,AUSTRALIA
ANDREWS, RK
;
BOOTH, WJ
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV SYDNEY,WESTMEAD CTR,THROMBOSIS & CARDIOVASC DIS RES CTR,DEPT MED,WESTMEAD,NSW 2145,AUSTRALIA
BOOTH, WJ
;
GORMAN, JJ
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV SYDNEY,WESTMEAD CTR,THROMBOSIS & CARDIOVASC DIS RES CTR,DEPT MED,WESTMEAD,NSW 2145,AUSTRALIA
GORMAN, JJ
;
CASTALDI, PA
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV SYDNEY,WESTMEAD CTR,THROMBOSIS & CARDIOVASC DIS RES CTR,DEPT MED,WESTMEAD,NSW 2145,AUSTRALIA
CASTALDI, PA
;
BERNDT, MC
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV SYDNEY,WESTMEAD CTR,THROMBOSIS & CARDIOVASC DIS RES CTR,DEPT MED,WESTMEAD,NSW 2145,AUSTRALIA
BERNDT, MC
.
BIOCHEMISTRY,
1989,
28
(21)
:8317
-8326
[6]
Molecular mechanisms of platelet adhesion and activation
[J].
Andrews, RK
论文数:
0
引用数:
0
h-index:
0
机构:
BAKER MED RES INST, HAZEL & PIP APPEL VASC BIOL LAB, PRAHRAN, VIC 3181, AUSTRALIA
Andrews, RK
;
Lopez, JA
论文数:
0
引用数:
0
h-index:
0
机构:
BAKER MED RES INST, HAZEL & PIP APPEL VASC BIOL LAB, PRAHRAN, VIC 3181, AUSTRALIA
Lopez, JA
;
Berndt, MC
论文数:
0
引用数:
0
h-index:
0
机构:
BAKER MED RES INST, HAZEL & PIP APPEL VASC BIOL LAB, PRAHRAN, VIC 3181, AUSTRALIA
Berndt, MC
.
INTERNATIONAL JOURNAL OF BIOCHEMISTRY & CELL BIOLOGY,
1997,
29
(01)
:91
-105
[7]
Binding of purified 14-3-3 ζ signaling protein to discrete amino acid sequences within the cytoplasmic domain of the platelet membrane glycoprotein Ib-IX-V complex
[J].
Andrews, RK
论文数:
0
引用数:
0
h-index:
0
机构:
Baker Med Res Inst, Hazel & Pip Appel Vasc Biol Lab, Prahran, Vic 3181, Australia
Baker Med Res Inst, Hazel & Pip Appel Vasc Biol Lab, Prahran, Vic 3181, Australia
Andrews, RK
;
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