Granular cell tumor of the neurohypophysis: report of a case with unusual age presentation

被引:28
作者
Benites, PR
Sakamoto, D
Machuca, TN
Serapiao, MJ
Ditzel, L
Torres, LFB
机构
[1] Univ Fed Parana, Hosp Clin, Dept Pathol, BR-80060900 Curitiba, Parana, Brazil
[2] Univ Fed Parana, Hosp Clin, Dept Neurosurg, BR-80060900 Curitiba, Parana, Brazil
关键词
granular cell tumor; neurohypophysis; central precocious puberty;
D O I
10.1007/s00428-005-1229-z
中图分类号
R36 [病理学];
学科分类号
100104 [病理学与病理生理学];
摘要
Granular cell tumor (GCT) usually occurs as a solitary, small, nodular tumor and rarely grows to a sufficient size to present symptoms. The tumor is more prevalent in female adults. The authors report a case of an 8-year-old boy with GCT of the neurohypophysis presenting with central precocious puberty. Few cases of symptomatic GCT have been reported in the literature, none of them in a patient in the first decade of life. Clinical picture, histopathological features, and histogenesis of GCT of neurohypophysis are discussed.
引用
收藏
页码:649 / 652
页数:4
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