Status epilepticus and venous infarction in Sturge-Weber syndrome

被引：20

作者：

Coley, SC

Britton, J

Clarke, A

机构：

[1] Atkinson Morleys Hosp, Dept Neuroradiol, London SW20 0NE, England

[2] Atkinson Morleys Hosp, Dept Neurol, London SW20 0NE, England

来源：

CHILDS NERVOUS SYSTEM | 1998年 / 14卷 / 12期

关键词：

Sturge-Weber syndrome; venous hypertension; cerebral infarction; status epilepticus; dementia;

D O I：

10.1007/s003810050299

中图分类号：

R74 [神经病学与精神病学];

学科分类号：

摘要：

Sturge-Weber syndrome (SWS) is a neurocutaneous disorder that is typically associated with progressive neurological deterioration. We describe a 12-year-old girl with SWS who suffered a permanent cerebral insult as the result of a period of protracted status epilepticus. The case illustrates the unique susceptibility of patients with SWS to uncontrolled venous hypertension and emphasises the need for optimal seizure control and preservation of venous outflow. We discuss the relevance of our observations to haemodynamic concepts of neurological decline in SWS.

引用

页码：693 / 696

页数：4

共 9 条

[1]

ALEXANDER GL, 1960, STURGEWEBER SYNDROME

[2] CEREBRAL VENOUS DRAINAGE PATTERN OF STURGE-WEBER SYNDROME [J].