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Domino hepatic transplantation in maple syrup urine disease
被引:30
作者
:
Barshop, BA
论文数:
0
引用数:
0
h-index:
0
机构:
Univ Calif San Diego, La Jolla, CA 92093 USA
Univ Calif San Diego, La Jolla, CA 92093 USA
Barshop, BA
[
1
]
Khanna, A
论文数:
0
引用数:
0
h-index:
0
机构:
Univ Calif San Diego, La Jolla, CA 92093 USA
Univ Calif San Diego, La Jolla, CA 92093 USA
Khanna, A
[
1
]
机构
:
[1]
Univ Calif San Diego, La Jolla, CA 92093 USA
来源
:
NEW ENGLAND JOURNAL OF MEDICINE
|
2005年
/ 353卷
/ 22期
关键词
:
D O I
:
10.1056/NEJM200512013532220
中图分类号
:
R5 [内科学];
学科分类号
:
1002
[临床医学]
;
100201
[内科学]
;
摘要
:
引用
收藏
页码:2410 / 2411
页数:2
相关论文
共 5 条
[1]
Branched-chain L-amino acid metabolism in classical maple syrup urine disease after orthotopic liver transplantation
[J].
Bodner-Leidecker, A
论文数:
0
引用数:
0
h-index:
0
机构:
Deutsch Diabet Forschungsinst, Klin Biochim, D-40225 Dusseldorf, Germany
Bodner-Leidecker, A
;
Wendel, U
论文数:
0
引用数:
0
h-index:
0
机构:
Deutsch Diabet Forschungsinst, Klin Biochim, D-40225 Dusseldorf, Germany
Wendel, U
;
Saudubray, JM
论文数:
0
引用数:
0
h-index:
0
机构:
Deutsch Diabet Forschungsinst, Klin Biochim, D-40225 Dusseldorf, Germany
Saudubray, JM
;
Schadewaldt, P
论文数:
0
引用数:
0
h-index:
0
机构:
Deutsch Diabet Forschungsinst, Klin Biochim, D-40225 Dusseldorf, Germany
Schadewaldt, P
.
JOURNAL OF INHERITED METABOLIC DISEASE,
2000,
23
(08)
:805
-818
[2]
PRACTICAL METHODS TO ESTIMATE WHOLE-BODY LEUCINE OXIDATION IN MAPLE SYRUP URINE DISEASE
[J].
ELSAS, LJ
论文数:
0
引用数:
0
h-index:
0
机构:
BAYLOR COLL MED,USDA ARS,CHILDRENS NUTR RES CTR,DEPT PEDIAT,HOUSTON,TX 77030
BAYLOR COLL MED,USDA ARS,CHILDRENS NUTR RES CTR,DEPT PEDIAT,HOUSTON,TX 77030
ELSAS, LJ
;
ELLERINE, NP
论文数:
0
引用数:
0
h-index:
0
机构:
BAYLOR COLL MED,USDA ARS,CHILDRENS NUTR RES CTR,DEPT PEDIAT,HOUSTON,TX 77030
BAYLOR COLL MED,USDA ARS,CHILDRENS NUTR RES CTR,DEPT PEDIAT,HOUSTON,TX 77030
ELLERINE, NP
;
KLEIN, PD
论文数:
0
引用数:
0
h-index:
0
机构:
BAYLOR COLL MED,USDA ARS,CHILDRENS NUTR RES CTR,DEPT PEDIAT,HOUSTON,TX 77030
BAYLOR COLL MED,USDA ARS,CHILDRENS NUTR RES CTR,DEPT PEDIAT,HOUSTON,TX 77030
KLEIN, PD
.
PEDIATRIC RESEARCH,
1993,
33
(05)
:445
-451
[3]
Kaplan P., 1997, Journal of Inherited Metabolic Disease, V20, P37
[4]
Mazariegos G, 2005, PEDIATR TRANSPLANT, V9, P49
[5]
Liver transplantation in maple syrup urine disease
[J].
Wendel, U
论文数:
0
引用数:
0
h-index:
0
机构:
Univ Dusseldorf, Kinderklin, Med Einrichtungen, D-40225 Dusseldorf, Germany
Wendel, U
;
Saudubray, JM
论文数:
0
引用数:
0
h-index:
0
机构:
Univ Dusseldorf, Kinderklin, Med Einrichtungen, D-40225 Dusseldorf, Germany
Saudubray, JM
;
Bodner, A
论文数:
0
引用数:
0
h-index:
0
机构:
Univ Dusseldorf, Kinderklin, Med Einrichtungen, D-40225 Dusseldorf, Germany
Bodner, A
;
Schadewaldt, P
论文数:
0
引用数:
0
h-index:
0
机构:
Univ Dusseldorf, Kinderklin, Med Einrichtungen, D-40225 Dusseldorf, Germany
Schadewaldt, P
.
EUROPEAN JOURNAL OF PEDIATRICS,
1999,
158
(Suppl 2)
:S60
-S64
←
1
→
共 5 条
[1]
Branched-chain L-amino acid metabolism in classical maple syrup urine disease after orthotopic liver transplantation
[J].
Bodner-Leidecker, A
论文数:
0
引用数:
0
h-index:
0
机构:
Deutsch Diabet Forschungsinst, Klin Biochim, D-40225 Dusseldorf, Germany
Bodner-Leidecker, A
;
Wendel, U
论文数:
0
引用数:
0
h-index:
0
机构:
Deutsch Diabet Forschungsinst, Klin Biochim, D-40225 Dusseldorf, Germany
Wendel, U
;
Saudubray, JM
论文数:
0
引用数:
0
h-index:
0
机构:
Deutsch Diabet Forschungsinst, Klin Biochim, D-40225 Dusseldorf, Germany
Saudubray, JM
;
Schadewaldt, P
论文数:
0
引用数:
0
h-index:
0
机构:
Deutsch Diabet Forschungsinst, Klin Biochim, D-40225 Dusseldorf, Germany
Schadewaldt, P
.
JOURNAL OF INHERITED METABOLIC DISEASE,
2000,
23
(08)
:805
-818
[2]
PRACTICAL METHODS TO ESTIMATE WHOLE-BODY LEUCINE OXIDATION IN MAPLE SYRUP URINE DISEASE
[J].
ELSAS, LJ
论文数:
0
引用数:
0
h-index:
0
机构:
BAYLOR COLL MED,USDA ARS,CHILDRENS NUTR RES CTR,DEPT PEDIAT,HOUSTON,TX 77030
BAYLOR COLL MED,USDA ARS,CHILDRENS NUTR RES CTR,DEPT PEDIAT,HOUSTON,TX 77030
ELSAS, LJ
;
ELLERINE, NP
论文数:
0
引用数:
0
h-index:
0
机构:
BAYLOR COLL MED,USDA ARS,CHILDRENS NUTR RES CTR,DEPT PEDIAT,HOUSTON,TX 77030
BAYLOR COLL MED,USDA ARS,CHILDRENS NUTR RES CTR,DEPT PEDIAT,HOUSTON,TX 77030
ELLERINE, NP
;
KLEIN, PD
论文数:
0
引用数:
0
h-index:
0
机构:
BAYLOR COLL MED,USDA ARS,CHILDRENS NUTR RES CTR,DEPT PEDIAT,HOUSTON,TX 77030
BAYLOR COLL MED,USDA ARS,CHILDRENS NUTR RES CTR,DEPT PEDIAT,HOUSTON,TX 77030
KLEIN, PD
.
PEDIATRIC RESEARCH,
1993,
33
(05)
:445
-451
[3]
Kaplan P., 1997, Journal of Inherited Metabolic Disease, V20, P37
[4]
Mazariegos G, 2005, PEDIATR TRANSPLANT, V9, P49
[5]
Liver transplantation in maple syrup urine disease
[J].
Wendel, U
论文数:
0
引用数:
0
h-index:
0
机构:
Univ Dusseldorf, Kinderklin, Med Einrichtungen, D-40225 Dusseldorf, Germany
Wendel, U
;
Saudubray, JM
论文数:
0
引用数:
0
h-index:
0
机构:
Univ Dusseldorf, Kinderklin, Med Einrichtungen, D-40225 Dusseldorf, Germany
Saudubray, JM
;
Bodner, A
论文数:
0
引用数:
0
h-index:
0
机构:
Univ Dusseldorf, Kinderklin, Med Einrichtungen, D-40225 Dusseldorf, Germany
Bodner, A
;
Schadewaldt, P
论文数:
0
引用数:
0
h-index:
0
机构:
Univ Dusseldorf, Kinderklin, Med Einrichtungen, D-40225 Dusseldorf, Germany
Schadewaldt, P
.
EUROPEAN JOURNAL OF PEDIATRICS,
1999,
158
(Suppl 2)
:S60
-S64
←
1
→