Transplantation for factor VII deficiency

被引：14

作者：

Levi, D

Pefkarou, A

Fort, JA

DeFaria, W

Tzakis, AG

机构：

[1] Univ Miami, Jackson Mem Med Ctr, Dept Surg, Div Transplantat, Miami, FL 33152 USA

[2] Miami Childrens Hosp, Dept Hematol Oncol, Miami, FL USA

来源：

TRANSPLANTATION | 2001年 / 72卷 / 11期

关键词：

D O I：

10.1097/00007890-200112150-00021

中图分类号：

R392 [医学免疫学]; Q939.91 [免疫学];

学科分类号：

100102 ;

摘要：

Factor VII deficiency is a serious, potentially lethal disorder of blood coagulation caused by a defect in hepatic factor VII synthesis. We report two children, sisters, both with severe, recurrent hemorrhagic complications from factor VII deficiency, successfully treated with orthotopic liver transplantation. Postoperatively, they remain symptom free with normal coagulation profiles.

引用

页码：1836 / 1837

页数：2

共 10 条

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[2]

BONTEMPO FA, 1987, BLOOD, V69, P1721

[3]

CASELLA JF, 1988, LANCET, V1, P435

[4]

FAKHRY SM, 1997, TXB SURG, P118