Molecular and cellular mechanisms of cardiac arrhythmias

被引:765
作者
Keating, MT [1 ]
Sanguinetti, MC
机构
[1] Harvard Univ, Sch Med,Childrens Hosp, Howard Hughes Med Inst, Dept Cell Biol, Boston, MA 02115 USA
[2] Univ Utah, Hlth Sci Ctr, Dept Med,Eccles Program Human Mol Biol & Genet, Div Cardiol, Salt Lake City, UT 84112 USA
关键词
D O I
10.1016/S0092-8674(01)00243-4
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
[No abstract available]
引用
收藏
页码:569 / 580
页数:12
相关论文
共 71 条
[1]   MiRP1 forms IKr potassium channels with HERG and is associated with cardiac arrhythmia [J].
Abbott, GW ;
Sesti, F ;
Splawski, I ;
Buck, ME ;
Lehmann, WH ;
Timothy, KW ;
Keating, MT ;
Goldstein, SAN .
CELL, 1999, 97 (02) :175-187
[2]  
Abildskov J. A., 1991, J CARDIOVASC ELECTR, V2, P355, DOI 10.1111/j.1540-8167.1991.tb01332.x
[3]  
Ashcroft F.M., 2000, Ion Channels and Disease
[4]   K(v)LQT1 and IsK (minK) proteins associate to form the I-Ks cardiac potassium current [J].
Barhanin, J ;
Lesage, F ;
Guillemare, E ;
Fink, M ;
Lazdunski, M ;
Romey, G .
NATURE, 1996, 384 (6604) :78-80
[5]   MOLECULAR MECHANISM FOR AN INHERITED CARDIAC-ARRHYTHMIA [J].
BENNETT, PB ;
YAZAWA, K ;
MAKITA, N ;
GEORGE, AL .
NATURE, 1995, 376 (6542) :683-685
[6]  
Brugada J, 1997, CIRCULATION, V96, P841
[7]   A pore mutation in a novel KQT-like potassium channel gene in an idiopathic epilepsy family [J].
Charlier, C ;
Singh, NA ;
Ryan, SG ;
Lewis, TB ;
Reus, BE ;
Leach, RJ ;
Leppert, M .
NATURE GENETICS, 1998, 18 (01) :53-55
[8]   Long QT syndrome-associated mutations in the Per-Arnt-Sim (PAS) domain of HERG potassium channels accelerate channel deactivation [J].
Chen, J ;
Zou, AR ;
Splawski, I ;
Keating, MT ;
Sanguinetti, MC .
JOURNAL OF BIOLOGICAL CHEMISTRY, 1999, 274 (15) :10113-10118
[9]   Genetic basis and molecular mechanism for idiopathic: ventricular fibrillation [J].
Chen, QY ;
Kirsch, GE ;
Zhang, DM ;
Brugada, R ;
Brugada, J ;
Brugada, P ;
Potenza, D ;
Moya, A ;
Borggrefe, M ;
Breithardt, G ;
Ortiz-Lopez, R ;
Wang, Z ;
Antzelevitch, C ;
O'Brien, RE ;
Schulze-Bahr, E ;
Keating, MT ;
Towbin, JA ;
Wang, Q .
NATURE, 1998, 392 (6673) :293-296
[10]   Genetically defined therapy of inherited long-QT syndrome - Correction of abnormal repolarization by potassium [J].
Compton, SJ ;
Lux, RL ;
Ramsey, MR ;
Strelich, KR ;
Sanguinetti, MC ;
Green, LS ;
Keating, MT ;
Mason, JW .
CIRCULATION, 1996, 94 (05) :1018-1022