Factor V: a combination of Dr Jekyll and Mr Hyde

被引:179
作者
Mann, KG
Kalafatis, M
机构
[1] Univ Vermont, Coll Med, Dept Biochem, Burlington, VT 05405 USA
[2] Cleveland Clin Fdn, Lerner Res Inst, Dept Mol Cardiol, Cleveland, OH 44195 USA
[3] Cleveland State Univ, Dept Chem, Cleveland, OH 44115 USA
关键词
D O I
10.1182/blood-2002-01-0290
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:20 / 30
页数:11
相关论文
共 170 条
[1]  
Alhenc-Gelas M, 1999, THROMB HAEMOSTASIS, V81, P193
[2]   INCREASED RISK OF VENOUS THROMBOSIS IN CARRIERS OF HEREDITARY PROTEIN-C DEFICIENCY DEFECT [J].
ALLAART, CF ;
POORT, SR ;
ROSENDAAL, FR ;
REITSMA, PH ;
BERTINA, RM ;
BRIET, E .
LANCET, 1993, 341 (8838) :134-138
[3]   Molecular mechanisms of activated protein C resistance - Properties of factor V isolated from an individual with homozygosity for the Arg(506) to Gin mutation in the factor V gene [J].
Aparicio, C ;
Dahlback, B .
BIOCHEMICAL JOURNAL, 1996, 313 :467-472
[4]   An antifibrinolytic mechanism describing the prothrombotic effect associated with factor V-Leiden [J].
Bajzar, L ;
Kalafatis, M ;
Simioni, P ;
Tracy, PB .
JOURNAL OF BIOLOGICAL CHEMISTRY, 1996, 271 (38) :22949-22952
[5]  
BAJZAR L, 1993, J BIOL CHEM, V268, P8608
[6]   PURIFICATION AND CHARACTERIZATION OF TAFI, A THROMBIN-ACTIVABLE FIBRINOLYSIS INHIBITOR [J].
BAJZAR, L ;
MANUEL, R ;
NESHEIM, ME .
JOURNAL OF BIOLOGICAL CHEMISTRY, 1995, 270 (24) :14477-14484
[7]   A factor V genetic component differing from factor V R506Q contributes to the activated protein C resistance phenotype [J].
Bernardi, F ;
Faioni, EM ;
Castoldi, E ;
Lunghi, B ;
Castaman, G ;
Sacchi, E ;
Mannucci, PM .
BLOOD, 1997, 90 (04) :1552-1557
[8]  
Bertina RM, 2000, THROMB HAEMOSTASIS, V83, P360
[9]   MUTATION IN BLOOD-COAGULATION FACTOR-V ASSOCIATED WITH RESISTANCE TO ACTIVATED PROTEIN-C [J].
BERTINA, RM ;
KOELEMAN, BPC ;
KOSTER, T ;
ROSENDAAL, FR ;
DIRVEN, RJ ;
DERONDE, H ;
VANDERVELDEN, PA ;
REITSMA, PH .
NATURE, 1994, 369 (6475) :64-67
[10]   GENERATION OF PROTHROMBIN-CONVERTING ACTIVITY AND THE EXPOSURE OF PHOSPHATIDYLSERINE AT THE OUTER SURFACE OF PLATELETS [J].
BEVERS, EM ;
COMFURIUS, P ;
VANRIJN, JLML ;
HEMKER, HC ;
ZWAAL, RFA .
EUROPEAN JOURNAL OF BIOCHEMISTRY, 1982, 122 (02) :429-436