Heritable diseases of the blood vessels

被引：15

作者：

Baxter, BT ^{[1
]}

机构：

[1] Univ Nebraska Med Ctr, Dept Surg & Pathol, Omaha, NE 68132 USA

来源：

CARDIOVASCULAR PATHOLOGY | 2005年 / 14卷 / 04期

关键词：

aorta; dissection; aneurysm; Marfan syndrome; Ehlers-Danlos syndrome; bicuspid valve; nonsyndromic familial aortic dissection;

D O I：

10.1016/j.carpath.2005.04.003

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Four inherited disorders known to affect major arteries will be discussed, including Marfan syndrome (MS), Ehlers-Danlos syndrome (EDS), bicuspid aortic valve (BAV) and nonsyndromic familial aortic dissection. Recent advances in understanding their pathophysiology are presented, and how this knowledge impacts on diagnosis, prevention and treatment is discussed. (c) 2005 Elsevier Inc. All rights reserved.

引用

页码：185 / 188

页数：4

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