共 34 条
Update in cystic fibrosis 2006
被引:29
作者:

Accurso, Frank J.
论文数: 0 引用数: 0
h-index: 0
机构: Childrens Hosp, Denver, CO 80218 USA
机构:
[1] Childrens Hosp, Denver, CO 80218 USA
[2] Mike McMorris Cyst Fibrosis Care & Res Ctr, Denver, CO USA
[3] Univ Colorado, Hlth Sci Ctr, Dept Pediat, Denver, CO 80202 USA
关键词:
D O I:
10.1164/rccm.200701-160UP
中图分类号:
R4 [临床医学];
学科分类号:
1002 ;
100602 ;
摘要:
[No abstract available]
引用
收藏
页码:754 / 757
页数:4
相关论文
共 34 条
[1]
Multicenter randomized controlled trial of withdrawal of inhaled corticosteroids in cystic fibrosis
[J].
Balfour-Lynn, Ian M.
;
Lees, Belinda
;
Hall, Pippa
;
Phillips, Gillian
;
Khan, Mohammed
;
Flather, Marcus
;
Elborn, J. Stuart
.
AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE,
2006, 173 (12)
:1356-1362

Balfour-Lynn, Ian M.
论文数: 0 引用数: 0
h-index: 0
机构: Royal Brompton Hosp, Dept Paediat Resp Med, London SW3 6LY, England

Lees, Belinda
论文数: 0 引用数: 0
h-index: 0
机构: Royal Brompton Hosp, Dept Paediat Resp Med, London SW3 6LY, England

Hall, Pippa
论文数: 0 引用数: 0
h-index: 0
机构: Royal Brompton Hosp, Dept Paediat Resp Med, London SW3 6LY, England

Phillips, Gillian
论文数: 0 引用数: 0
h-index: 0
机构: Royal Brompton Hosp, Dept Paediat Resp Med, London SW3 6LY, England

Khan, Mohammed
论文数: 0 引用数: 0
h-index: 0
机构: Royal Brompton Hosp, Dept Paediat Resp Med, London SW3 6LY, England

Flather, Marcus
论文数: 0 引用数: 0
h-index: 0
机构: Royal Brompton Hosp, Dept Paediat Resp Med, London SW3 6LY, England

Elborn, J. Stuart
论文数: 0 引用数: 0
h-index: 0
机构: Royal Brompton Hosp, Dept Paediat Resp Med, London SW3 6LY, England
[2]
Risk factors for death of patients with cystic fibrosis awaiting lung transplantation
[J].
Belkin, RA
;
Henig, NR
;
Singer, LG
;
Chaparro, C
;
Rubenstein, RC
;
Xie, SX
;
Yee, JY
;
Kotloff, RM
;
Lipson, DA
;
Bunin, GR
.
AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE,
2006, 173 (06)
:659-666

Belkin, RA
论文数: 0 引用数: 0
h-index: 0
机构: Univ Penn, Med Ctr, Ctr Clin Epidemiol & Biostat, Div Pulm, Philadelphia, PA 19104 USA

Henig, NR
论文数: 0 引用数: 0
h-index: 0
机构: Univ Penn, Med Ctr, Ctr Clin Epidemiol & Biostat, Div Pulm, Philadelphia, PA 19104 USA

Singer, LG
论文数: 0 引用数: 0
h-index: 0
机构: Univ Penn, Med Ctr, Ctr Clin Epidemiol & Biostat, Div Pulm, Philadelphia, PA 19104 USA

Chaparro, C
论文数: 0 引用数: 0
h-index: 0
机构: Univ Penn, Med Ctr, Ctr Clin Epidemiol & Biostat, Div Pulm, Philadelphia, PA 19104 USA

Rubenstein, RC
论文数: 0 引用数: 0
h-index: 0
机构: Univ Penn, Med Ctr, Ctr Clin Epidemiol & Biostat, Div Pulm, Philadelphia, PA 19104 USA

Xie, SX
论文数: 0 引用数: 0
h-index: 0
机构: Univ Penn, Med Ctr, Ctr Clin Epidemiol & Biostat, Div Pulm, Philadelphia, PA 19104 USA

Yee, JY
论文数: 0 引用数: 0
h-index: 0
机构: Univ Penn, Med Ctr, Ctr Clin Epidemiol & Biostat, Div Pulm, Philadelphia, PA 19104 USA

Kotloff, RM
论文数: 0 引用数: 0
h-index: 0
机构: Univ Penn, Med Ctr, Ctr Clin Epidemiol & Biostat, Div Pulm, Philadelphia, PA 19104 USA

Lipson, DA
论文数: 0 引用数: 0
h-index: 0
机构: Univ Penn, Med Ctr, Ctr Clin Epidemiol & Biostat, Div Pulm, Philadelphia, PA 19104 USA

Bunin, GR
论文数: 0 引用数: 0
h-index: 0
机构: Univ Penn, Med Ctr, Ctr Clin Epidemiol & Biostat, Div Pulm, Philadelphia, PA 19104 USA
[3]
Relative contribution of genetic and nongenetic modifiers to intestinal obstruction in cystic fibrosis
[J].
Blackman, Scott M.
;
Deering-Brose, Rebecca
;
McWilliams, Rita
;
Naughton, Kathleen
;
Coleman, Barbara
;
Lai, Teresa
;
Algire, Marilyn
;
Beck, Suzanne
;
Hoover-Fong, Julie
;
Hamosh, Ada
;
Fallin, M. Daniele
;
West, Kristen
;
Arking, Dan E.
;
Chakravarti, Aravinda
;
Cutler, David J.
;
Cutting, Garry R.
.
GASTROENTEROLOGY,
2006, 131 (04)
:1030-1039

Blackman, Scott M.
论文数: 0 引用数: 0
h-index: 0
机构: Johns Hopkins Univ, Sch Med, McKusick Nathans Inst Genet Med, Baltimore, MD 21218 USA

Deering-Brose, Rebecca
论文数: 0 引用数: 0
h-index: 0
机构: Johns Hopkins Univ, Sch Med, McKusick Nathans Inst Genet Med, Baltimore, MD 21218 USA

McWilliams, Rita
论文数: 0 引用数: 0
h-index: 0
机构: Johns Hopkins Univ, Sch Med, McKusick Nathans Inst Genet Med, Baltimore, MD 21218 USA

Naughton, Kathleen
论文数: 0 引用数: 0
h-index: 0
机构: Johns Hopkins Univ, Sch Med, McKusick Nathans Inst Genet Med, Baltimore, MD 21218 USA

Coleman, Barbara
论文数: 0 引用数: 0
h-index: 0
机构: Johns Hopkins Univ, Sch Med, McKusick Nathans Inst Genet Med, Baltimore, MD 21218 USA

Lai, Teresa
论文数: 0 引用数: 0
h-index: 0
机构: Johns Hopkins Univ, Sch Med, McKusick Nathans Inst Genet Med, Baltimore, MD 21218 USA

Algire, Marilyn
论文数: 0 引用数: 0
h-index: 0
机构: Johns Hopkins Univ, Sch Med, McKusick Nathans Inst Genet Med, Baltimore, MD 21218 USA

Beck, Suzanne
论文数: 0 引用数: 0
h-index: 0
机构: Johns Hopkins Univ, Sch Med, McKusick Nathans Inst Genet Med, Baltimore, MD 21218 USA

Hoover-Fong, Julie
论文数: 0 引用数: 0
h-index: 0
机构: Johns Hopkins Univ, Sch Med, McKusick Nathans Inst Genet Med, Baltimore, MD 21218 USA

Hamosh, Ada
论文数: 0 引用数: 0
h-index: 0
机构: Johns Hopkins Univ, Sch Med, McKusick Nathans Inst Genet Med, Baltimore, MD 21218 USA

Fallin, M. Daniele
论文数: 0 引用数: 0
h-index: 0
机构: Johns Hopkins Univ, Sch Med, McKusick Nathans Inst Genet Med, Baltimore, MD 21218 USA

West, Kristen
论文数: 0 引用数: 0
h-index: 0
机构: Johns Hopkins Univ, Sch Med, McKusick Nathans Inst Genet Med, Baltimore, MD 21218 USA

Arking, Dan E.
论文数: 0 引用数: 0
h-index: 0
机构: Johns Hopkins Univ, Sch Med, McKusick Nathans Inst Genet Med, Baltimore, MD 21218 USA

Chakravarti, Aravinda
论文数: 0 引用数: 0
h-index: 0
机构: Johns Hopkins Univ, Sch Med, McKusick Nathans Inst Genet Med, Baltimore, MD 21218 USA

Cutler, David J.
论文数: 0 引用数: 0
h-index: 0
机构: Johns Hopkins Univ, Sch Med, McKusick Nathans Inst Genet Med, Baltimore, MD 21218 USA

Cutting, Garry R.
论文数: 0 引用数: 0
h-index: 0
机构: Johns Hopkins Univ, Sch Med, McKusick Nathans Inst Genet Med, Baltimore, MD 21218 USA
[4]
Ion and fluid transport properties of small airways in cystic fibrosis
[J].
Blouquit, Sabine
;
Regnier, Agathe
;
Dannhoffer, Luc
;
Fermanian, Christophe
;
Naline, Emmanuel
;
Boucher, Richard
;
Chinet, Thierry
.
AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE,
2006, 174 (03)
:299-305

Blouquit, Sabine
论文数: 0 引用数: 0
h-index: 0
机构: Univ Versailles, UPRES EA220, Dept Pathol, Boulogne, France

Regnier, Agathe
论文数: 0 引用数: 0
h-index: 0
机构: Univ Versailles, UPRES EA220, Dept Pathol, Boulogne, France

Dannhoffer, Luc
论文数: 0 引用数: 0
h-index: 0
机构: Univ Versailles, UPRES EA220, Dept Pathol, Boulogne, France

Fermanian, Christophe
论文数: 0 引用数: 0
h-index: 0
机构: Univ Versailles, UPRES EA220, Dept Pathol, Boulogne, France

Naline, Emmanuel
论文数: 0 引用数: 0
h-index: 0
机构: Univ Versailles, UPRES EA220, Dept Pathol, Boulogne, France

Boucher, Richard
论文数: 0 引用数: 0
h-index: 0
机构: Univ Versailles, UPRES EA220, Dept Pathol, Boulogne, France

Chinet, Thierry
论文数: 0 引用数: 0
h-index: 0
机构: Univ Versailles, UPRES EA220, Dept Pathol, Boulogne, France
[5]
Study of a novel pancreatic enzyme replacement therapy in pancreatic insufficient subjects with cystic fibrosis
[J].
Borowitz, Drucy
;
Goss, Christopher H.
;
Limauro, Stacey
;
Konstan, Michael W.
;
Blake, Kathryn
;
Casey, Susan
;
Quittner, Alexandra L.
;
Murray, Frederick T.
.
JOURNAL OF PEDIATRICS,
2006, 149 (05)
:658-662

Borowitz, Drucy
论文数: 0 引用数: 0
h-index: 0
机构: SUNY Buffalo, Womens & Childrens Hosp Buffalo, Div Pediat Pulmonol, Buffalo, NY 14222 USA

Goss, Christopher H.
论文数: 0 引用数: 0
h-index: 0
机构: SUNY Buffalo, Womens & Childrens Hosp Buffalo, Div Pediat Pulmonol, Buffalo, NY 14222 USA

Limauro, Stacey
论文数: 0 引用数: 0
h-index: 0
机构: SUNY Buffalo, Womens & Childrens Hosp Buffalo, Div Pediat Pulmonol, Buffalo, NY 14222 USA

Konstan, Michael W.
论文数: 0 引用数: 0
h-index: 0
机构: SUNY Buffalo, Womens & Childrens Hosp Buffalo, Div Pediat Pulmonol, Buffalo, NY 14222 USA

Blake, Kathryn
论文数: 0 引用数: 0
h-index: 0
机构: SUNY Buffalo, Womens & Childrens Hosp Buffalo, Div Pediat Pulmonol, Buffalo, NY 14222 USA

Casey, Susan
论文数: 0 引用数: 0
h-index: 0
机构: SUNY Buffalo, Womens & Childrens Hosp Buffalo, Div Pediat Pulmonol, Buffalo, NY 14222 USA

Quittner, Alexandra L.
论文数: 0 引用数: 0
h-index: 0
机构: SUNY Buffalo, Womens & Childrens Hosp Buffalo, Div Pediat Pulmonol, Buffalo, NY 14222 USA

Murray, Frederick T.
论文数: 0 引用数: 0
h-index: 0
机构: SUNY Buffalo, Womens & Childrens Hosp Buffalo, Div Pediat Pulmonol, Buffalo, NY 14222 USA
[6]
Cystic fibrosis transmembrane conductance regulator function is suppressed in cigarette smokers
[J].
Cantin, Andre M.
;
Hanrahan, John W.
;
Bilodeau, Ginette
;
Ellis, Lynda
;
Dupuis, Annie
;
Liao, Jie
;
Zielenski, Julian
;
Durie, Peter
.
AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE,
2006, 173 (10)
:1139-1144

Cantin, Andre M.
论文数: 0 引用数: 0
h-index: 0
机构: Univ Sherbrooke, Fac Med, Pulm Res Unit, Sherbrooke, PQ J1H 5N4, Canada

Hanrahan, John W.
论文数: 0 引用数: 0
h-index: 0
机构: Univ Sherbrooke, Fac Med, Pulm Res Unit, Sherbrooke, PQ J1H 5N4, Canada

Bilodeau, Ginette
论文数: 0 引用数: 0
h-index: 0
机构: Univ Sherbrooke, Fac Med, Pulm Res Unit, Sherbrooke, PQ J1H 5N4, Canada

Ellis, Lynda
论文数: 0 引用数: 0
h-index: 0
机构: Univ Sherbrooke, Fac Med, Pulm Res Unit, Sherbrooke, PQ J1H 5N4, Canada

论文数: 引用数:
h-index:
机构:

Liao, Jie
论文数: 0 引用数: 0
h-index: 0
机构: Univ Sherbrooke, Fac Med, Pulm Res Unit, Sherbrooke, PQ J1H 5N4, Canada

Zielenski, Julian
论文数: 0 引用数: 0
h-index: 0
机构: Univ Sherbrooke, Fac Med, Pulm Res Unit, Sherbrooke, PQ J1H 5N4, Canada

Durie, Peter
论文数: 0 引用数: 0
h-index: 0
机构: Univ Sherbrooke, Fac Med, Pulm Res Unit, Sherbrooke, PQ J1H 5N4, Canada
[7]
Quantifying pulmonary inflammation in cystic fibrosis with positron emission tomography
[J].
Chen, Delphine L.
;
Ferkol, Thomas W.
;
Mintun, Mark A.
;
Pittman, Jessica E.
;
Rosenbluth, Daniel B.
;
Schuster, Daniel P.
.
AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE,
2006, 173 (12)
:1363-1369

Chen, Delphine L.
论文数: 0 引用数: 0
h-index: 0
机构: Washington Univ, Sch Med, Dept Radiol, St Louis, MO 63110 USA

Ferkol, Thomas W.
论文数: 0 引用数: 0
h-index: 0
机构: Washington Univ, Sch Med, Dept Radiol, St Louis, MO 63110 USA

Mintun, Mark A.
论文数: 0 引用数: 0
h-index: 0
机构: Washington Univ, Sch Med, Dept Radiol, St Louis, MO 63110 USA

Pittman, Jessica E.
论文数: 0 引用数: 0
h-index: 0
机构: Washington Univ, Sch Med, Dept Radiol, St Louis, MO 63110 USA

Rosenbluth, Daniel B.
论文数: 0 引用数: 0
h-index: 0
机构: Washington Univ, Sch Med, Dept Radiol, St Louis, MO 63110 USA

Schuster, Daniel P.
论文数: 0 引用数: 0
h-index: 0
机构: Washington Univ, Sch Med, Dept Radiol, St Louis, MO 63110 USA
[8]
Long term effects of azithromycin in patients with cystic fibrosis: a double blind, placebo controlled trial
[J].
Clement, A.
;
Tamalet, A.
;
Leroux, E.
;
Ravilly, S.
;
Fauroux, B.
;
Jais, J-P
.
THORAX,
2006, 61 (10)
:895-902

Clement, A.
论文数: 0 引用数: 0
h-index: 0
机构: Univ Paris 06, Hop Trousseau, Pediat Pulm Dept, INSERM,U719, F-75571 Paris 12, France

Tamalet, A.
论文数: 0 引用数: 0
h-index: 0
机构: Univ Paris 06, Hop Trousseau, Pediat Pulm Dept, INSERM,U719, F-75571 Paris 12, France

Leroux, E.
论文数: 0 引用数: 0
h-index: 0
机构: Univ Paris 06, Hop Trousseau, Pediat Pulm Dept, INSERM,U719, F-75571 Paris 12, France

Ravilly, S.
论文数: 0 引用数: 0
h-index: 0
机构: Univ Paris 06, Hop Trousseau, Pediat Pulm Dept, INSERM,U719, F-75571 Paris 12, France

论文数: 引用数:
h-index:
机构:

Jais, J-P
论文数: 0 引用数: 0
h-index: 0
机构: Univ Paris 06, Hop Trousseau, Pediat Pulm Dept, INSERM,U719, F-75571 Paris 12, France
[9]
Cystic fibrosis since 1938
[J].
Davis, PB
.
AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE,
2006, 173 (05)
:475-482

Davis, PB
论文数: 0 引用数: 0
h-index: 0
机构:
Case Western Reserve Univ, Sch Med, Rainbow Babies & Childrens Hosp, Dept Pediat, Cleveland, OH 44106 USA Case Western Reserve Univ, Sch Med, Rainbow Babies & Childrens Hosp, Dept Pediat, Cleveland, OH 44106 USA
[10]
Mucus clearance and lung function in cystic fibrosis with hypertonic saline
[J].
Donaldson, SH
;
Bennett, WD
;
Zeman, KL
;
Knowles, MR
;
Tarran, R
;
Boucher, RC
.
NEW ENGLAND JOURNAL OF MEDICINE,
2006, 354 (03)
:241-250

Donaldson, SH
论文数: 0 引用数: 0
h-index: 0
机构: Univ N Carolina, Chapel Hill Cyst Fibrosis Res & Treatment Ctr, Chapel Hill, NC USA

Bennett, WD
论文数: 0 引用数: 0
h-index: 0
机构: Univ N Carolina, Chapel Hill Cyst Fibrosis Res & Treatment Ctr, Chapel Hill, NC USA

Zeman, KL
论文数: 0 引用数: 0
h-index: 0
机构: Univ N Carolina, Chapel Hill Cyst Fibrosis Res & Treatment Ctr, Chapel Hill, NC USA

Knowles, MR
论文数: 0 引用数: 0
h-index: 0
机构: Univ N Carolina, Chapel Hill Cyst Fibrosis Res & Treatment Ctr, Chapel Hill, NC USA

Tarran, R
论文数: 0 引用数: 0
h-index: 0
机构: Univ N Carolina, Chapel Hill Cyst Fibrosis Res & Treatment Ctr, Chapel Hill, NC USA

Boucher, RC
论文数: 0 引用数: 0
h-index: 0
机构: Univ N Carolina, Chapel Hill Cyst Fibrosis Res & Treatment Ctr, Chapel Hill, NC USA