Polyunsaturated fatty acids reverse the lysosomal storage and accumulation of subunit 9 of mitochondrial F1F0-ATP synthase in cultured lymphoblasts from patients with Batten disease

被引：6

作者：

Bennett, MJ

Boriack, RL

Boustany, RM

机构：

[1] UNIV TEXAS,SW MED CTR,DEPT PATHOL & PEDIAT,DALLAS,TX

[2] DUKE UNIV,MED CTR,DEPT PEDIAT,DURHAM,NC 27710

[3] DUKE UNIV,MED CTR,DEPT NEUROL,DURHAM,NC 27710

[4] DUKE UNIV,MED CTR,DEPT NEUROBIOL,DURHAM,NC 27710

来源：

JOURNAL OF INHERITED METABOLIC DISEASE | 1997年 / 20卷 / 03期

关键词：

D O I：

10.1023/A:1005387608456

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

引用

页码：457 / 460

页数：4

共 10 条

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