Intrapartum airway management for giant fetal neck masses: The EXIT (ex utero intrapartum treatment) procedure

被引:126
作者
Liechty, KW
Crombleholme, TM
Flake, AW
Morgan, MA
Kurth, CD
Hubbard, AM
Adzick, NC
机构
[1] CHILDRENS HOSP,CTR FETAL DIAG & TREATMENT,DEPT SURG,PHILADELPHIA,PA 19104
[2] CHILDRENS HOSP,CTR FETAL DIAG & TREATMENT,DEPT ANESTHESIOL,PHILADELPHIA,PA 19104
[3] CHILDRENS HOSP,CTR FETAL DIAG & TREATMENT,DEPT RADIOL,PHILADELPHIA,PA 19104
[4] HOSP UNIV PENN,DEPT OBSTET & GYNECOL,PHILADELPHIA,PA 19104
[5] UNIV PENN,SCH MED,PHILADELPHIA,PA 19104
关键词
cervical teratoma; lymphangioma; EXIT procedure; perinatal management; fetal surgery;
D O I
10.1016/S0002-9378(97)70285-0
中图分类号
R71 [妇产科学];
学科分类号
100211 ;
摘要
OBJECTIVE: Our goal was to review our experience with the EXIT (ex utero intrapartum treatment) procedure in the management of five cases with life-threatening fetal neck masses. STUDY DESIGN: We present a retrospective review of prenatal presentation and course, diagnostic accuracy of imaging studies, intraoperative management, complications, and outcomes. RESULTS: Polyhydramnios was the initial presenting symptom in three of five fetuses with a mean gestational age of 25 +/- 6 weeks. Preterm labor occurred in two patients. Fetal magnetic resonance imaging provided accurate diagnosis in all four cases whereas conventional ultrasonography led to the diagnosis in four of five cases. The mean duration of EXIT was 28 +/- 22 minutes. The mean Venous cord blood gas values were pH 7.22 +/- 0.05, Pco(2) 61 +/- 11 mm Hg, and Po-2 42 +/- 8 mm Hg. In four of five cases an airway was successfully secured. CONCLUSIONS: The EXIT procedure provides up to 1 hour of good uteroplacental support and is the procedure of choice to secure an airway in the fetus with a giant neck mass.
引用
收藏
页码:870 / 874
页数:5
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