The new variant form of Creutzfeldt-Jakob disease: A novel prion protein amyloid disorder

被引:7
作者
Ironside, JW
机构
来源
AMYLOID-INTERNATIONAL JOURNAL OF EXPERIMENTAL AND CLINICAL INVESTIGATION | 1997年 / 4卷 / 01期
关键词
D O I
10.3109/13506129708995272
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
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页码:66 / 69
页数:4
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共 15 条
[1]   Transmission dynamics and epidemiology of BSE in British cattle [J].
Anderson, RM ;
Donnelly, CA ;
Ferguson, NM ;
Woolhouse, MEJ ;
Watt, CJ ;
Udy, HJ ;
MaWhinney, S ;
Dunstan, SP ;
Southwood, TRE ;
Wilesmith, JW ;
Ryan, JBM ;
Hoinville, LJ ;
Hillerton, JE ;
Austin, AR ;
Wells, GAH .
NATURE, 1996, 382 (6594) :779-788
[2]   EXPERIMENTAL TRANSMISSION OF BSE AND SCRAPIE TO THE COMMON MARMOSET [J].
BAKER, HF ;
RIDLEY, RM ;
WELLS, GAH .
VETERINARY RECORD, 1993, 132 (16) :403-406
[3]   NEUROPATHOLOGY OF SPONGIFORM ENCEPHALOPATHIES IN HUMANS [J].
BELL, JE ;
IRONSIDE, JW .
BRITISH MEDICAL BULLETIN, 1993, 49 (04) :738-777
[4]  
BRUCE ME, 1996, PRION DIS, P223
[5]   New variant of Creutzfeldt-Jakob disease in a 26-year-old French man [J].
Chazot, G ;
Broussolle, E ;
Lapras, C ;
Blattler, T ;
Aguzzi, A ;
Kopp, N .
LANCET, 1996, 347 (9009) :1181-1181
[6]   Molecular analysis of prion strain variation and the aetiology of 'new variant' CJD [J].
Collinge, J ;
Sidle, KCL ;
Meads, J ;
Ironside, J ;
Hill, AF .
NATURE, 1996, 383 (6602) :685-690
[7]   UNALTERED SUSCEPTIBILITY TO BSE IN TRANSGENIC MICE EXPRESSING HUMAN PRION PROTEIN [J].
COLLINGE, J ;
PALMER, MS ;
SIDLE, KCL ;
HILL, AF ;
GOWLAND, I ;
MEADS, J ;
ASANTE, E ;
BRADLEY, R ;
DOEY, LJ ;
LANTOS, PL .
NATURE, 1995, 378 (6559) :779-783
[8]   NEUROPATHOLOGICAL PHENOTYPE AND PRION PROTEIN GENOTYPE CORRELATION IN SPORADIC CREUTZFELDT-JAKOB-DISEASE [J].
DESILVA, R ;
IRONSIDE, JW ;
MCCARDLE, L ;
ESMONDE, T ;
BELL, J ;
WILL, R ;
WINDL, O ;
DEMPSTER, M ;
ESTIBEIRO, P ;
LATHE, R .
NEUROSCIENCE LETTERS, 1994, 179 (1-2) :50-52
[9]  
Fraser H., 1979, Aspects of slow and persistent virus infections, P30
[10]   Prion protein amyloidosis [J].
Ghetti, B ;
Piccardo, P ;
Frangione, B ;
Bugiani, O ;
Giaccone, G ;
Young, K ;
Prelli, F ;
Farlow, MR ;
Dlouhy, SR ;
Tagliavini, F .
BRAIN PATHOLOGY, 1996, 6 (02) :127-145