Lymphatic dysplasia in a neonate with Noonan's syndrome

被引:12
作者
Bloomfield, FH [1 ]
Hadden, W [1 ]
Gunn, TR [1 ]
机构
[1] NATL WOMENS HOSP,DEPT RADIOL,AUCKLAND,NEW ZEALAND
关键词
Neonatal Period; Hydrops Fetalis; Lymphatic Abnormality; Nonimmune Hydrops; Lymphatic Dysplasia;
D O I
10.1007/s002470050139
中图分类号
R72 [儿科学];
学科分类号
100202 [儿科学];
摘要
We present the case of a patient with Noonan's syndrome and massive nonimmune hydrops fetalis in whom lymphangiography was performed in the neonatal period. This demonstrated generalised lymphatic dysplasia, and we suggest a mechanism by which the lymphatic abnormalities in Noonan's syndrome may arise.
引用
收藏
页码:321 / 323
页数:3
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