Calcitonin treatment in osteoectasia with hyperphosphatasia (juvenile Paget's disease):: radiographic changes after treatment

被引:18
作者
Tüysüz, B
Mercimek, S
Üngür, S
Deniz, M
机构
[1] Univ Istanbul, Carrahpasa Fac Med, Dept Paediat, Div Genet & Teratol, Istanbul, Turkey
[2] Haseki Hosp, Dept Paediat, Istanbul, Turkey
关键词
Alkaline Phosphatase; Calcitonin; Elevated Serum; Radiological Finding; Serum Alkaline Phosphatase;
D O I
10.1007/s002470050708
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Osteoectasia with hyperphosphatasia is a rare skeletal disorder, characterised by demineralisation and expansion of tubular bones and elevated serum alkaline phosphatase. We present a girl diagnosed as having osteoectasia with hyperphosphatasia who had swelling of phalanges of both hands and motor retardation. She was treated with synthetic human calcitonin. Clinical and radiological findings showed remarkable improvement after 2 years' treatment.
引用
收藏
页码:838 / 841
页数:4
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