Erythromelalgia: an endothelial disorder responsive to sodium nitroprusside

被引:18
作者
Chan, MKH [1 ]
Tucker, AT [1 ]
Madden, S [1 ]
Golding, CEM [1 ]
Atherton, DJ [1 ]
Dillon, MJ [1 ]
机构
[1] St Bartholomews Hosp, Clin Microvasc Unit, London, England
关键词
D O I
10.1136/adc.87.3.229
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Erythromelalgia is an unusual syndrome of painful vasodilation. Aetiopathology is probably different in children and adults. Presentation can be severe and associated with hypertension. Dramatic benefit from infused nitroprusside suggests the disorder could represent a dysfunctional endothelium.
引用
收藏
页码:229 / 230
页数:2
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