Wernicke encephalopathy and Creutzfeldt-Jakob disease

被引：12

作者：

Bertrand, A. ^{[2
]}

Brandel, J. P. ^{[3
]}

Grignon, Y. ^{[4
]}

Sazdovitch, V. ^{[2
,3
]}

Seilhean, D. ^{[2
]}

Faucheux, B. ^{[3
]}

Privat, N. ^{[3
]}

Brault, J. L. ^{[5
]}

Vital, A. ^{[6
]}

Uro-Coste, E. ^{[7
]}

Pluot, M. ^{[8
]}

Chapon, F. ^{[9
]}

Maurage, C. A. ^{[10
]}

Letournel, F. ^{[11
]}

Vespignani, H. ^{[12
]}

Place, G. ^{[13
]}

Degos, C. F. ^{[14
]}

Peoc'h, K. ^{[15
,16
]}

Haik, S. ^{[2
,3
]}

Hauw, J. J. ^{[1
,2
]}

机构：

[1] GH Pitie Salpetriere, Lab Neuropathol R Escourolle, F-75651 Paris 13, France

[2] Hop La Pitie Salpetriere, APHP, Ctr Natl Reference ATNC InVS, Fac Med Pierre & Marie Curie,Lab Neuropathol R Es, F-75651 Paris 13, France

[3] INSERM, Avenir Team, Paris, France

[4] CHR Metz Thionville, Hop Bel Air, Anat Pathol Lab, F-57100 Thionville, France

[5] Hop Louis Pasteur, F-28018 Chartres, France

[6] Hop Pellegrin, Dept Neuropathol, F-33076 Bordeaux, France

[7] Hop Rangueil, Serv Anat & Cytol Pathol, F-31403 Toulouse 4, France

[8] Hop Robert Debre, Lab Cent Anat & Cytol Pathol, F-51092 Reims, France

[9] CHU Caen, Serv Neurol, F-14033 Caen, France

[10] CHU Lille, F-59037 Lille, France

[11] CHU Angers, Dept Pathol Cellulaire & Tissulaire, F-49933 Angers, France

[12] Hopital Cent, Serv Neurol, F-45053 Nancy, France

[13] Ctr Accueil & Soins Hosp Nanterre, Serv Reanimat, F-92014 Nanterre, France

[14] Hop St Joseph, F-75674 Paris 14, France

[15] Hop Lariboisiere, APHP, Serv Biochim & Biol Mol, F-75475 Paris, France

[16] Fac Pharm Paris 5, EA 3621, Paris, France

来源：

JOURNAL OF NEUROLOGY | 2009年 / 256卷 / 06期

关键词：

Creutzfeldt-Jakob; Wernicke encephalopathy; Diagnosis of dementia; CLINICAL SPECTRUM; DIAGNOSIS; CRITERIA;

D O I：

10.1007/s00415-009-5038-1

中图分类号：

R74 [神经病学与精神病学];

学科分类号：

摘要：

We assessed the prevalence of Wernicke encephalopathy (WE) in all 657 cases suspected of Creutzfeldt-Jakob (CJD) referred from 2001 to 2006 to the French Neuropathology Network of CJD. Clinical, biological and imaging data were reviewed when the diagnosis of WE was made at autopsy. No CJD was found in five cases suspected of sporadic CJD. In these five cases, myoclonus had been observed in four, CSF 14-3-3 protein in two. In 14 other cases, WE was combined with CJD, 13 of which were sporadic. These belonged mainly to the molecular variants of sporadic CJD associated with a long duration of disease. This stresses the necessity of remaining alert to the diagnosis of WE when CJD is suspected.

引用

页码：904 / 909

页数：6

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