Right ventricular dysfunction in congenitally corrected transposition of the great arteries

被引:62
作者
Hornung, TS [1 ]
Bernard, EJ [1 ]
Celermajer, DS [1 ]
Jaeggi, E [1 ]
Howman-Giles, RB [1 ]
Chard, RB [1 ]
Hawker, RE [1 ]
机构
[1] Royal Alexandra Hosp Children, Dept Nucl Med, Adolph Basser Cardiac Inst, Sydney, NSW, Australia
关键词
D O I
10.1016/S0002-9149(99)00516-0
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Although right ventricular (RV) dysfunction is an important complication in subjects with congenitally corrected transposition of the great arteries, its pathogenesis is poorly understood. We assessed the role of RV myocardial perfusion and found perfusion defects at rest in all 20 patients, involving 4.6 +/- 2.3 of a total of 12 segments; the extent of the resting perfusion defects correlated inversely with the RV ejection fraction.
引用
收藏
页码:1116 / +
页数:5
相关论文
共 11 条
[1]   CONGENITALLY CORRECTED TRANSPOSITION OF GREAT ARTERIES - MORPHOLOGIC STUDY OF 32 CASES [J].
ALLWORK, SP ;
BENTALL, HH ;
BECKER, AE ;
CAMERON, H ;
GERLIS, LM ;
WILKINSON, JL ;
ANDERSON, RH .
AMERICAN JOURNAL OF CARDIOLOGY, 1976, 38 (07) :910-923
[2]   MAXIMAL OXYGEN INTAKE AND NOMOGRAPHIC ASSESSMENT OF FUNCTIONAL AEROBIC IMPAIRMENT IN CARDIOVASCULAR DISEASE [J].
BRUCE, RA ;
KUSUMI, F ;
HOSMER, D .
AMERICAN HEART JOURNAL, 1973, 85 (04) :546-562
[3]   BRUCE TREADMILL TEST IN CHILDREN - NORMAL VALUES IN A CLINIC POPULATION [J].
CUMMING, GR ;
EVERATT, D ;
HASTMAN, L .
AMERICAN JOURNAL OF CARDIOLOGY, 1978, 41 (01) :69-75
[4]   LONG-TERM FUNCTION OF THE MORPHOLOGIC RIGHT VENTRICLE IN ADULT PATIENTS WITH CORRECTED TRANSPOSITION OF THE GREAT-ARTERIES [J].
DIMAS, AP ;
MOODIE, DS ;
STERBA, R ;
GILL, CC .
AMERICAN HEART JOURNAL, 1989, 118 (03) :526-530
[5]   ASSESSMENT OF VENTRICULAR SIZE AND FUNCTION IN CONGENITALLY CORRECTED TRANSPOSITION OF THE GREAT-ARTERIES [J].
GRAHAM, TP ;
PARRISH, MD ;
BOUCEK, RJ ;
BOERTH, RC ;
BREITWESER, JA ;
THOMPSON, S ;
ROBERTSON, RM ;
MORGAN, JR ;
FRIESINGER, GC .
AMERICAN JOURNAL OF CARDIOLOGY, 1983, 51 (02) :244-251
[6]   Myocardial perfusion defects and associated systemic ventricular dysfunction in congenitally corrected transposition of the great arteries [J].
Hornung, TS ;
Bernard, EJ ;
Jaeggi, ET ;
Howman-Giles, RB ;
Celermajer, DS ;
Hawker, RE .
HEART, 1998, 80 (04) :322-326
[7]   LONG-TERM SURVIVAL IN AGED PATIENTS WITH CORRECTED TRANSPOSITION OF THE GREAT-ARTERIES [J].
IKEDA, U ;
FURUSE, M ;
SUZUKI, O ;
KIMURA, K ;
SEKIGUCHI, H ;
SHIMADA, K .
CHEST, 1992, 101 (05) :1382-1385
[8]  
Losekoot TG, 1987, PAEDIAT CARDIOLOGY, P867
[9]  
MELEROPITA A, N ENGL J MED, V334, P866
[10]  
PRESBITERO P, 1995, BRIT HEART J, V74, P57