Childhood chronic immune thrombocytopenic purpura (ITP)

被引:32
作者
Blanchette, V [1 ]
机构
[1] Hosp Sick Children, Dept Hematol Oncol, Toronto, ON M5G 1X8, Canada
关键词
chronic immune thrombocytopenic purpura (ITP); childhood; splenectomy;
D O I
10.1054/blre.2001.0176
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Chronic immune thrombocytopenic purpura (ITP) develops in approximately 20% of children with acute ITR Treatment requires differentiating the truly idiopathic state from thrombocytopenias associated with other disorders. Treatment is recommended in cases where platelet counts drop below 20 x 10(9)/L. Therapeutic options include corticosteroids, intravenous immunoglobulin TG(IVIg), and anti-D, as well as splenectomy. The benefits and disadvantages of each modality are reviewed, as well as the management of postsplenectomy failures. (C) 2002, Elsevier Science Ltd. All rights reserved.
引用
收藏
页码:23 / 26
页数:4
相关论文
共 24 条
[1]   ACCESSORY SPLEEN COMPROMISING RESPONSE TO SPLENECTOMY FOR IDIOPATHIC THROMBOCYTOPENIC PURPURA [J].
AMBRIZ, P ;
MUNOZ, R ;
QUINTANAR, E ;
SIGLER, L ;
AVILES, A ;
PIZZUTO, J .
RADIOLOGY, 1985, 155 (03) :793-796
[2]   RESPONSE OF RESISTANT IDIOPATHIC THROMBOCYTOPENIC PURPURA TO PULSED HIGH-DOSE DEXAMETHASONE THERAPY [J].
ANDERSEN, JC .
NEW ENGLAND JOURNAL OF MEDICINE, 1994, 330 (22) :1560-1564
[3]   A MULTICENTER STUDY OF THE TREATMENT OF CHILDHOOD CHRONIC IDIOPATHIC THROMBOCYTOPENIC PURPURA WITH ANTI-D [J].
ANDREW, M ;
BLANCHETTE, VS ;
ADAMS, M ;
ALI, K ;
BARNARD, D ;
CHAN, KW ;
DEVEBER, LB ;
ESSELTINE, D ;
ISRAELS, S ;
KORBRINSKY, N ;
LUKE, B ;
MILNER, RA ;
WOLOSKI, BMR ;
VEGH, P .
JOURNAL OF PEDIATRICS, 1992, 120 (04) :522-527
[4]   URGENT TREATMENT OF IDIOPATHIC THROMBOCYTOPENIC PURPURA WITH SINGLE-DOSE GAMMA-GLOBULIN INFUSION FOLLOWED BY PLATELET TRANSFUSION [J].
BAUMANN, MA ;
MENITOVE, JE ;
ASTER, RH ;
ANDERSON, T .
ANNALS OF INTERNAL MEDICINE, 1986, 104 (06) :808-809
[5]   RANDOMIZED TRIAL OF INTRAVENOUS IMMUNOGLOBULIN-G, INTRAVENOUS ANTI-D, AND ORAL PREDNISONE IN CHILDHOOD ACUTE IMMUNE THROMBOCYTOPENIC PURPURA [J].
BLANCHETTE, V ;
IMBACH, P ;
ANDREW, M ;
ADAMS, M ;
MCMILLAN, J ;
WANG, E ;
MILNER, R ;
ALI, K ;
BARNARD, D ;
BERNSTEIN, M ;
CHAN, KW ;
ESSELTINE, D ;
DEVEBER, B ;
ISRAELS, S ;
KOBRINSKY, N ;
LUKE, B .
LANCET, 1994, 344 (8924) :703-707
[6]  
Blanchette V, 1998, SEMIN HEMATOL, V35, P36
[7]  
BLANCHETTE VS, 1992, SEMIN HEMATOL, V29, P72
[8]   A PROSPECTIVE, RANDOMIZED TRIAL OF HIGH-DOSE INTRAVENOUS IMMUNE GLOBULIN G THERAPY, ORAL PREDNISONE THERAPY, AND NO THERAPY IN CHILDHOOD ACUTE IMMUNE THROMBOCYTOPENIC PURPURA [J].
BLANCHETTE, VS ;
LUKE, B ;
ANDREW, M ;
SOMMERVILLENIELSEN, S ;
BARNARD, D ;
DEVEBER, B ;
GENT, M .
JOURNAL OF PEDIATRICS, 1993, 123 (06) :989-995
[9]   A trial of high-dose dexamethasone therapy for chronic idiopathic thrombocytopenic purpura in childhood [J].
BorgnaPignatti, C ;
Rugolotto, S ;
Nobili, B ;
Amendola, G ;
DeStefano, P ;
Maccario, R ;
Locatelli, F .
JOURNAL OF PEDIATRICS, 1997, 130 (01) :13-16
[10]  
Carcao MD, 1998, ACTA PAEDIATR, V87, P71