Mitochondrial damage: An important feature in a number of inborn errors of metabolism?

被引:22
作者
Heales, SJR
Bolanos, JP
Brand, MP
Clark, JB
Land, JM
机构
[1] UCL NATL HOSP NEUROL & NEUROSURG, DEPT CLIN BIOCHEM, LONDON WC1N 3BG, ENGLAND
[2] UNIV SALAMANCA, DEPT BIOCHEM & MOLEC BIOL, SALAMANCA, SPAIN
关键词
D O I
10.1007/BF01799414
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:140 / 142
页数:3
相关论文
共 8 条
[1]  
BOLANOS JP, 1995, J NEUROCHEM, V64, P1965
[2]  
HEALES SJR, 1995, NEUROCHEM RES, V20, P31
[3]   CA2+/CALMODULIN-DEPENDENT FORMATION OF HYDROGEN-PEROXIDE BY BRAIN NITRIC-OXIDE SYNTHASE [J].
HEINZEL, B ;
JOHN, M ;
KLATT, P ;
BOHME, E ;
MAYER, B .
BIOCHEMICAL JOURNAL, 1992, 281 :627-630
[4]  
JIAN A, 1991, P NATL ACAD SCI USA, V88, P1913
[5]  
MAYER B, 1995, N-S ARCH PHARMACOL, V351, P453
[6]  
MEISTER A, 1989, METABOLIC BASIS INHE, P855
[7]   CYTOCHROME-C OXIDASE AND CARDIOLIPIN ALTERATIONS IN RESPONSE TO SKELETAL-MUSCLE ISCHEMIA AND REPERFUSION [J].
SOUSSI, B ;
IDSTROM, JP ;
SCHERSTEN, T ;
BYLUNDFELLENIUS, AC .
ACTA PHYSIOLOGICA SCANDINAVICA, 1990, 138 (02) :107-114
[8]  
ZHANG Y, 1990, J BIOL CHEM, V265, P16330