Nonsecretory myeloma, immunoglobulin D myeloma, and plasma cell leukemia

被引:144
作者
Bladé, J [1 ]
Kyle, RA
机构
[1] Inst Invest Biomed August Pi & Sunyez, Dept Hematol, Hosp & Clin, Barcelona, Spain
[2] Mayo Clin & Mayo Fdn, Div Hematol & Internal Med, Rochester, MN 55905 USA
[3] Mayo Clin & Mayo Grad Sch Med, Rochester, MN 55901 USA
关键词
D O I
10.1016/S0889-8588(05)70125-8
中图分类号
R73 [肿瘤学];
学科分类号
100214 ;
摘要
Nonsecretory myeloma is characterized by the absence of detectable monoclonal protein in serum and urine. It accounts for approximately 2% of all patients with multiple myeloma. Immunoglobulin D myeloma accounts for about 2% of patients with myeloma. Extramedullary plasmacytoma, lambda light chain, and amyloidosis are more common in this disorder. Plasma cell leukemia occurs in about 2% of patients with myeloma. It is primary in 60%, and in the remainder it is secondary as a part of the terminal phase of multiple myeloma. It is more aggressive than multiple myeloma and has a higher frequency of extramedullary involvement, anemia, thrombocytopenia, hypercalcemia, and renal failure.
引用
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页码:1259 / +
页数:15
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