Intestinal microvillous atrophy in a patient with Down syndrome and aganglionic megacolon

被引：5

作者：

Martinez, MA

Egea, AS

López, JM

Benítez, EM

机构：

[1] Hosp Univ 12 Octubre, Dept Pathol, Madrid, Spain

[2] Hosp Univ 12 Octubre, Dept Paediat, Madrid, Spain

来源：

ULTRASTRUCTURAL PATHOLOGY | 2002年 / 26卷 / 01期

关键词：

Down syndrome; hirschprung disease; intestinal microvillous atrophy;

D O I：

10.1080/01913120252934323

中图分类号：

TH742 [显微镜];

学科分类号：

摘要：

Intestinal microvillous disorders are an uncommon cause of severe diarrhea, with very poor prognosis. The authors report the case of a female infant with Down syndrome, aganglionic megacolon, severe diarrhea, and jejuna! biopsy with ultrastructural changes consistent with microvillous atrophy. The patient condition improved after a colostomy performed in the setting of the treatment of Hirschprung disease.

引用

页码：41 / 45

页数：5

共 31 条

[1] MICROVILLOUS INCLUSION DISEASE - THE IMPORTANCE OF ELECTRON-MICROSCOPY FOR DIAGNOSIS [J].