From Charcot to SOD1: Mechanisms of selective motor neuron death in ALS

被引:198
作者
Cleveland, DW [1 ]
机构
[1] Univ Calif San Diego, Ludwig Inst Canc Res, La Jolla, CA 92093 USA
[2] Univ Calif San Diego, Dept Med, La Jolla, CA 92093 USA
[3] Univ Calif San Diego, Dept Neurosci, La Jolla, CA 92093 USA
关键词
D O I
10.1016/S0896-6273(00)81108-3
中图分类号
Q189 [神经科学];
学科分类号
071006 ;
摘要
[No abstract available]
引用
收藏
页码:515 / 520
页数:6
相关论文
共 40 条
  • [1] Deletions of the heavy neurofilament subunit tail in amyotrophic lateral sclerosis
    Al-Chalabi, A
    Andersen, PM
    Nilsson, P
    Chioza, B
    Andersson, JL
    Russ, C
    Shaw, CE
    Powell, JF
    Leigh, PN
    [J]. HUMAN MOLECULAR GENETICS, 1999, 8 (02) : 157 - 164
  • [2] Andrus PK, 1998, J NEUROCHEM, V71, P2041
  • [3] ALS, SOD AND PEROXYNITRITE
    BECKMAN, JS
    CARSON, M
    SMITH, CD
    KOPPENOL, WH
    [J]. NATURE, 1993, 364 (6438) : 584 - 584
  • [4] SUPEROXIDE-DISMUTASE-1 WITH MUTATIONS LINKED TO FAMILIAL AMYOTROPHIC-LATERAL-SCLEROSIS POSSESSES SIGNIFICANT ACTIVITY
    BORCHELT, DR
    LEE, MK
    SLUNT, HS
    GUARNIERI, M
    XU, ZS
    WONG, PC
    BROWN, RH
    PRICE, DL
    SISODIA, SS
    CLEVELAND, DW
    [J]. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1994, 91 (17) : 8292 - 8296
  • [5] SUPEROXIDE-DISMUTASE ACTIVITY, OXIDATIVE DAMAGE, AND MITOCHONDRIAL ENERGY-METABOLISM IN FAMILIAL AND SPORADIC AMYOTROPHIC-LATERAL-SCLEROSIS
    BOWLING, AC
    SCHULZ, JB
    BROWN, RH
    BEAL, MF
    [J]. JOURNAL OF NEUROCHEMISTRY, 1993, 61 (06) : 2322 - 2325
  • [6] AMYOTROPHIC-LATERAL-SCLEROSIS - RECENT INSIGHTS FROM GENETICS AND TRANSGENIC MICE
    BROWN, RH
    [J]. CELL, 1995, 80 (05) : 687 - 692
  • [7] Up-regulation of protein chaperones preserves viability of cells expressing toxic Cu/Zn-superoxide dismutase mutants associated with amyotrophic lateral sclerosis
    Bruening, W
    Roy, J
    Giasson, B
    Figlewicz, DA
    Mushynski, WE
    Durham, HD
    [J]. JOURNAL OF NEUROCHEMISTRY, 1999, 72 (02) : 693 - 699
  • [8] Elevated free nitrotyrosine levels, but not protein-bound nitrotyrosine or hydroxyl radicals, throughout amyotrophic lateral sclerosis (ALS)-like disease implicate tyrosine nitration as an aberrant in vivo property of one familial ALS-linked superoxide dismutase 1 mutant
    Bruijn, LI
    Beal, MF
    Becher, MW
    Schulz, JB
    Wong, PC
    Price, DL
    Cleveland, DW
    [J]. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1997, 94 (14) : 7606 - 7611
  • [9] ALS-linked SOD1 mutant G85R mediates damage to astrocytes and promotes rapidly progressive disease with SOD1-containing inclusions
    Bruijn, LI
    Becher, MW
    Lee, MK
    Anderson, KL
    Jenkins, NA
    Copeland, NG
    Sisodia, SS
    Rothstein, JD
    Borchelt, DR
    Price, DL
    Cleveland, DW
    [J]. NEURON, 1997, 18 (02) : 327 - 338
  • [10] Aggregation and motor neuron toxicity of an ALS-linked SOD1 mutant independent from wild-type SOD1
    Bruijn, LI
    Houseweart, MK
    Kato, S
    Anderson, KL
    Anderson, SD
    Ohama, E
    Reaume, AG
    Scott, RW
    Cleveland, DW
    [J]. SCIENCE, 1998, 281 (5384) : 1851 - 1854