Significance at late ventricular potentials in myotonic dystrophy

被引:21
作者
Babuty, D
Fauchier, L
Tena-Carbi, D
Poret, P
Leche, J
Raynoud, M
Fauchier, JP
Cosnay, P
机构
[1] Fac Med, Dept Cardiol B, Tours, France
[2] Fac Med, Dept Neurol, Tours, France
[3] Fac Med, Dept Genet, Tours, France
关键词
D O I
10.1016/S0002-9149(99)00510-X
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
In 39 patients with myotonic dystrophy, we found a high percentage of infrahissian cardiac conduction abnormalities (51%) and late potentials (46%), whereas spontaneous and inducible ventricular arrhythmias were rare. These results suggest that the prolongation of QRSD and the duration of the low-amplitude signal on the signal-averaged electrocardiogram were related to delayed activation of the His and Purkinje tissue rather than true late potentials.
引用
收藏
页码:1099 / +
页数:4
相关论文
共 9 条
[1]  
BACARIELLO G, 1986, AM HEART J, V111, P413
[2]   STANDARDS FOR ANALYSIS OF VENTRICULAR LATE POTENTIALS USING HIGH-RESOLUTION OR SIGNAL-AVERAGED ELECTROCARDIOGRAPHY - A STATEMENT BY A TASK-FORCE-COMMITTEE OF THE EUROPEAN-SOCIETY-OF-CARDIOLOGY, THE AMERICAN-HEART-ASSOCIATION, AND THE AMERICAN-COLLEGE-OF-CARDIOLOGY [J].
BREITHARDT, G ;
CAIN, ME ;
ELSHERIF, N ;
FLOWERS, NC ;
HOMBACH, V ;
JANSE, M ;
SIMSON, MB ;
STEINBECK, G .
JOURNAL OF THE AMERICAN COLLEGE OF CARDIOLOGY, 1991, 17 (05) :999-1006
[3]   EFFECT OF CONDUCTION DEFECTS ON THE SIGNAL-AVERAGED ELECTROCARDIOGRAPHIC DETERMINATION OF LATE POTENTIALS [J].
BUCKINGHAM, TA ;
THESSEN, CC ;
STEVENS, LL ;
REDD, RM ;
KENNEDY, HL .
AMERICAN JOURNAL OF CARDIOLOGY, 1988, 61 (15) :1265-1271
[4]   Value of the electrocardiogram in determining cardiac events and mortality in myotonic dystrophy [J].
Colleran, JA ;
Hawley, RJ ;
Pinnow, EE ;
Kokkinos, PF ;
Fletcher, RD .
AMERICAN JOURNAL OF CARDIOLOGY, 1997, 80 (11) :1494-1497
[5]   CARDIAC CONDUCTION IN MYOTONIC-DYSTROPHY [J].
GRIGGS, RC ;
DAVIS, RJ ;
ANDERSON, DC ;
DOVE, JT .
AMERICAN JOURNAL OF MEDICINE, 1975, 59 (01) :37-42
[6]   VENTRICULAR LATE POTENTIALS IN MYOTONIC-DYSTROPHY [J].
MILNER, MR ;
HAWLEY, RJ ;
JACHIM, M ;
LINDSAY, J ;
FLETCHER, RD .
ANNALS OF INTERNAL MEDICINE, 1991, 115 (08) :607-613
[7]   CARDIAC INVOLVEMENT IN MYOTONIC MUSCULAR-DYSTROPHY [J].
MOORMAN, JR ;
COLEMAN, RE ;
PACKER, DL ;
KISSLO, JA ;
BELL, J ;
HETTLEMAN, BD ;
STAJICH, J ;
ROSES, AD .
MEDICINE, 1985, 64 (06) :371-387
[8]   NATURAL-HISTORY OF CONDUCTION SYSTEM DISEASE IN MYOTONIC MUSCULAR-DYSTROPHY AS DETERMINED BY SERIAL ELECTROPHYSIOLOGIC STUDIES [J].
PRYSTOWSKY, EN ;
PRITCHETT, ELC ;
ROSES, AD ;
GALLAGHER, J .
CIRCULATION, 1979, 60 (06) :1360-1364
[9]   UNSTABLE DNA MAY BE RESPONSIBLE FOR THE INCOMPLETE PENETRANCE OF THE MYOTONIC-DYSTROPHY PHENOTYPE [J].
SHELBOURNE, P ;
WINQVIST, R ;
KUNERT, E ;
DAVIES, J ;
LEISTI, J ;
THIELE, H ;
BACHMANN, H ;
BUXTON, J ;
WILLIAMSON, B ;
JOHNSON, K .
HUMAN MOLECULAR GENETICS, 1992, 1 (07) :467-473