The benefits of liver transplantation in glycogenosis type Ib

被引：22

作者：

Bhattacharya, K

Heaton, N

Rela, M

Walter, JH

Lee, PJ

机构：

[1] Great Ormond St Hosp Sick Children, Metab Unit, London WC1N 3JH, England

[2] Kings Coll Hosp London, Liver Unit, London, England

[3] Royal Manchester Childrens Hosp, Willink Biochem Genet Unit, Manchester M27 1HA, Lancs, England

来源：

JOURNAL OF INHERITED METABOLIC DISEASE | 2004年 / 27卷 / 04期

关键词：

D O I：

10.1023/B:BOLI.0000037400.49488.20

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

There are few reports of liver transplantation in glycogenosis type Ib (GSD Ib). We present two cases who had dramatic catch-up growth and reduced infections after transplantation, despite persistent neutropenia.

引用

页码：539 / 540

页数：2

共 3 条

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