Peroxisomes in human fibroblasts have a basic pH

被引:96
作者
Dansen, TB
Wirtz, KWA
Wanders, RJA
Pap, EHW
机构
[1] Univ Utrecht, Dept Biochem Lipids, Ctr Biomembranes & Lipid Enzymol, Inst Biomembranes, NL-3508 TB Utrecht, Netherlands
[2] Univ Amsterdam, Acad Med Ctr, Dept Clin Chem, NL-1105 AZ Amsterdam, Netherlands
[3] Univ Amsterdam, Acad Med Ctr, Dept Paediat, NL-1105 AZ Amsterdam, Netherlands
关键词
D O I
10.1038/71375
中图分类号
Q2 [细胞生物学];
学科分类号
071009 ; 090102 ;
摘要
[No abstract available]
引用
收藏
页码:51 / 53
页数:3
相关论文
共 16 条
[1]   Alkyl-dihydroxyacetonephosphate synthase - Fate in peroxisome biogenesis disorders and identification of the point mutation underlying a single enzyme deficiency [J].
de Vet, ECJM ;
Ijlst, L ;
Oostheim, W ;
Wanders, RJA ;
van den Bosch, H .
JOURNAL OF BIOLOGICAL CHEMISTRY, 1998, 273 (17) :10296-10301
[2]   Multiple PEX genes are required for proper subcellular distribution and stability of Pex5p, the PTS1 receptor: Evidence that PTS1 protein import is mediated by a cycling receptor [J].
Dodt, G ;
Gould, SJ .
JOURNAL OF CELL BIOLOGY, 1996, 135 (06) :1763-1774
[3]   MUTATIONS IN THE PTS1 RECEPTOR GENE, PXR1, DEFINE COMPLEMENTATION GROUP-2 OF THE PEROXISOME BIOGENESIS DISORDERS [J].
DODT, G ;
BRAVERMAN, N ;
WONG, C ;
MOSER, A ;
MOSER, HW ;
WATKINS, P ;
VALLE, D ;
GOULD, SJ .
NATURE GENETICS, 1995, 9 (02) :115-125
[4]   A CONSERVED TRIPEPTIDE SORTS PROTEINS TO PEROXISOMES [J].
GOULD, SJ ;
KELLER, GA ;
HOSKEN, N ;
WILKINSON, J ;
SUBRAMANI, S .
JOURNAL OF CELL BIOLOGY, 1989, 108 (05) :1657-1664
[5]   IDP3 encodes a peroxisomal NADP-dependent isocitrate dehydrogenase required for the β-oxidation of unsaturated fatty acids [J].
Henke, B ;
Girzalsky, W ;
Berteaux-Lecellier, V ;
Erdmann, R .
JOURNAL OF BIOLOGICAL CHEMISTRY, 1998, 273 (06) :3702-3711
[6]   Identification of PAHX, a Refsum disease gene [J].
Mihalik, SJ ;
Morrell, JC ;
Kim, D ;
Sacksteder, KA ;
Watkins, PA ;
Gould, SJ .
NATURE GENETICS, 1997, 17 (02) :185-189
[7]   Rhizomelic chondrodysplasia punctata is a peroxisomal protein targeting disease caused by a non-functional PTS2 receptor [J].
Motley, AM ;
Hettema, EH ;
Hogenhout, EM ;
Brites, P ;
tenAsbroek, ALMA ;
Wijburg, FA ;
Baas, F ;
Heijmans, HS ;
Tabak, HF ;
Wanders, RJA ;
Distel, B .
NATURE GENETICS, 1997, 15 (04) :377-380
[8]   Components involved in peroxisome import, biogenesis, proliferation, turnover, and movement [J].
Subramani, S .
PHYSIOLOGICAL REVIEWS, 1998, 78 (01) :171-188
[9]   BIOCHEMISTRY OF PEROXISOMES [J].
VANDENBOSCH, H ;
SCHUTGENS, RBH ;
WANDERS, RJA ;
TAGER, JM .
ANNUAL REVIEW OF BIOCHEMISTRY, 1992, 61 :157-197
[10]   THE MEMBRANE OF PEROXISOMES IN SACCHAROMYCES-CEREVISIAE IS IMPERMEABLE TO NAD(H) AND ACETYL-COA UNDER IN-VIVO CONDITIONS [J].
VANROERMUND, CWT ;
ELGERSMA, Y ;
SINGH, N ;
WANDERS, RJA ;
TABAK, HF .
EMBO JOURNAL, 1995, 14 (14) :3480-3486