Neonatal cricopharyngeal achalasia - A case report

被引:5
作者
Raboei, E [1 ]
Luoma, R [1 ]
机构
[1] King Fahd Armed Forces Hosp, Dept Pediat Surg, Jeddah 21159, Saudi Arabia
关键词
congenital cricopharyngeal achalasia; cricopharyngeal myotomy;
D O I
10.1055/s-2008-1072341
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Primary neonatal cricopharyngeal achalasia due to a spastic cricopharyngeus muscle manifests itself with intractable feeding difficulties, nasal reflux, recurrent aspiration pneumonia and failure to thrive. There are very few reports of this condition in the literature. In the absence of anatomically demonstrable cause, these children are likely to be labelled as having an impairment of the central-nervous system. This in turn may result in long-term misery with ng-tube feeding, and eventually, the creation of a feeding gastrostomy. A minor operation - cricopharyngeal myotomy - has been shown to be safe and curative. It can be performed even if only limited preoperative diagnostic tools are available.
引用
收藏
页码:130 / 132
页数:3
相关论文
共 11 条
[1]   CRICOPHARYNGEAL ACHALASIA IN CHILDHOOD [J].
BISHOP, HC .
JOURNAL OF PEDIATRIC SURGERY, 1974, 9 (05) :775-778
[2]   CRICOPHARYNGEAL ACHALASIA AS A CAUSE OF RESPIRATORY DISTRESS IN INFANCY [J].
BLANK, RH ;
SILBIGER, M .
JOURNAL OF PEDIATRICS, 1972, 81 (01) :95-+
[3]   STRUCTURAL ABNORMALITIES OF THE CRICOPHARYNGEUS MUSCLE IN PATIENTS WITH PHARYNGEAL (ZENKERS) DIVERTICULUM [J].
COOK, IJ ;
BLUMBERGS, P ;
CASH, K ;
JAMIESON, GG ;
SHEARMAN, DJ .
JOURNAL OF GASTROENTEROLOGY AND HEPATOLOGY, 1992, 7 (06) :556-562
[4]  
FALCETTI D, 1995, 1 EUR C PAED SURG GR
[6]  
LAURIKAINEN E, 1992, EUR ARCH OTO-RHINO-L, V249, P216
[7]   CONGENITAL CRICOPHARYNGEAL ACHALASIA TREATMENT BY DILATATIONS [J].
LERNAU, OZ ;
SHERZER, E ;
MOGLE, P ;
NISSAN, S .
JOURNAL OF PEDIATRIC SURGERY, 1984, 19 (02) :202-203
[8]   TREATMENT OF DYSFUNCTION OF THE CRICOPHARYNGEAL MUSCLE WITH BOTULINUM A TOXIN - INTRODUCTION OF A NEW, NONINVASIVE METHOD [J].
SCHNEIDER, I ;
POTOTSCHNIG, C ;
THUMFART, WF ;
ECKEL, HE .
ANNALS OF OTOLOGY RHINOLOGY AND LARYNGOLOGY, 1994, 103 (01) :31-35
[9]   PRIMARY NEONATAL CRICOPHARYNGEAL ACHALASIA - A CASE-REPORT AND REVIEW OF THE LITERATURE [J].
SKINNER, MA ;
SHORTER, NA .
JOURNAL OF PEDIATRIC SURGERY, 1992, 27 (12) :1509-1511
[10]  
UTIAN HL, 1969, PEDIATRICS, V43, P402