Aberrant protein deposition and neurological disease

[1] Role of microglia and host prion protein in neurotoxicity of a prion protein fragment [J]. NATURE, 1996, 380 (6572) : 345 - 347

[2] ALS-linked SOD1 mutant G85R mediates damage to astrocytes and promotes rapidly progressive disease with SOD1-containing inclusions [J]. NEURON, 1997, 18 (02) : 327 - 338

[3] Truncated forms of the androgen receptor are associated with polyglutamine expansion in X-linked spinal and bulbar muscular atrophy [J]. HUMAN MOLECULAR GENETICS, 1998, 7 (01) : 121 - 127

[4] Evidence for proteasome involvement in polyglutamine disease:: localization to nuclear inclusions in SCA3/MJD and suppression of polyglutamine aggregation in vitro [J]. HUMAN MOLECULAR GENETICS, 1999, 8 (04) : 673 - 682

[5] Chaperone suppression of aggregation and altered subcellular proteasome localization imply protein misfolding in SCA1 [J]. NATURE GENETICS, 1998, 19 (02) : 148 - 154

[6] Formation of neuronal intranuclear inclusions underlies the neurological dysfunction in mice transgenic for the HD mutation [J]. CELL, 1997, 90 (03) : 537 - 548

[7] Selective neuronal targeting in prion disease [J]. NEURON, 1997, 19 (06) : 1337 - 1348

[8] Duvoisin RC, 1996, ADV NEUROL, V69, P33

[9] Cleavage of atrophin-1 at caspase site aspartic acid 109 modulates cytotoxicity [J]. JOURNAL OF BIOLOGICAL CHEMISTRY, 1999, 274 (13) : 8730 - 8736

[10] Gregori L, 1997, J BIOL CHEM, V272, P58

[1] Role of microglia and host prion protein in neurotoxicity of a prion protein fragment [J]. NATURE, 1996, 380 (6572) : 345 - 347

[2] ALS-linked SOD1 mutant G85R mediates damage to astrocytes and promotes rapidly progressive disease with SOD1-containing inclusions [J]. NEURON, 1997, 18 (02) : 327 - 338

[3] Truncated forms of the androgen receptor are associated with polyglutamine expansion in X-linked spinal and bulbar muscular atrophy [J]. HUMAN MOLECULAR GENETICS, 1998, 7 (01) : 121 - 127

[4] Evidence for proteasome involvement in polyglutamine disease:: localization to nuclear inclusions in SCA3/MJD and suppression of polyglutamine aggregation in vitro [J]. HUMAN MOLECULAR GENETICS, 1999, 8 (04) : 673 - 682

[5] Chaperone suppression of aggregation and altered subcellular proteasome localization imply protein misfolding in SCA1 [J]. NATURE GENETICS, 1998, 19 (02) : 148 - 154

[6] Formation of neuronal intranuclear inclusions underlies the neurological dysfunction in mice transgenic for the HD mutation [J]. CELL, 1997, 90 (03) : 537 - 548

[7] Selective neuronal targeting in prion disease [J]. NEURON, 1997, 19 (06) : 1337 - 1348

[8] Duvoisin RC, 1996, ADV NEUROL, V69, P33

[9] Cleavage of atrophin-1 at caspase site aspartic acid 109 modulates cytotoxicity [J]. JOURNAL OF BIOLOGICAL CHEMISTRY, 1999, 274 (13) : 8730 - 8736

[10] Gregori L, 1997, J BIOL CHEM, V272, P58